L.F. Menezes and L.F. Onuchic. Molecular and cellular pathogenesis of autosomal recessive polycystic kidney disease. Braz J Med Biol Res 2006; 39: 1537-1548. 

Figure 1. Renal pathology of autosomal recessive polycystic kidney disease. A, Kidney of a 2-year-old ARPKD-affected child. Macroscopically, the organ displays multiple small cysts on its surface and is severely enlarged, measuring ~15 cm in its longitudinal axis (Gift of Dr. Francisco Tibor Dénes). B, Drawing representing the diffuse and radial distribution of dilated collecting ducts throughout the cortex and medulla. C, ARPKD renal histology, showing dilation of collecting ducts.