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Cutaneous neonatal lupus with cutis marmorata telangiectatica congenita-like lesions* * Study carried out at the Medical School of Jundiaí (Faculdade de Medicina de Jundiaí - FMJ) - Jundiaí (SP), Brazil.

Lúpus cutâneo neonatal com lesões semelhantes à cutis marmorata telangiectatica congênita

Neonatal lupus is a rare disease caused by the transplacental transfer of maternal autoantibodies to the foetus, characterized by transient clinical manifestations such as cutaneous, haematological, and hepatobiliary events or permanent such as congenital heart block. The typical cutaneous manifestations include erythematous, scaly, annular or arched lesions on the face, with slight central atrophy and photosensitivy, clinically and histologically similar to subacute cutaneous lupus. However, in some cases, the lesions may resemble those in cutis marmorata telangiectatica congenita, although this phenomenon is rare and only eight such cases have been reported to date. We report a case of cutaneous neonatal lupus with atypical lesions on the limbs, which had a reddish-purple marbled appearance, resembling the lesions in cutis marmorata telangiectatica congenita.

Antibodies; Autoantibodies; Clinical diagnosis; Congenital, hereditary, and neonatal diseases and abnormalities; Diagnosis, differential; Lupus erythematosus, systemic


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