Acessibilidade / Reportar erro

Ophthalmic evaluation, treatment, and follow-up of two cases of incontinentia pigmenti

Avaliação oftalmológica, tratamento e seguimento de dois casos de incontinentia pigmenti

Incontinentia pigmenti (IP) is an X-linked dominant disorder affecting the skin, teeth, eyes, and central nervous system. Ocular changes are common and may lead to severe vision loss. We report on the ocular manifestations in two young girls with IP, with emphasis on the asymmetry of this condition in both eyes and associated retinal problems. The outcomes of laser treatment of the ischemic peripheral retina were good and resulted in stability of vision.

Incontinentia pigmenti/diagnosis; Incontinentia pigmenti/therapy; Laser therapy; Case reports


Conselho Brasileiro de Oftalmologia Rua Casa do Ator, 1117 - cj.21, 04546-004 São Paulo SP Brazil, Tel: 55 11 - 3266-4000, Fax: 55 11- 3171-0953 - São Paulo - SP - Brazil
E-mail: abo@cbo.com.br