ABSTRACT
Langerhans cell histiocytosis is the designated name for a spectrum of rare diseases that affects children from one- to three-years-old, which name refers to the proliferation of cells morphologically and immunophenotypically similar to the specialized dendritic cells of the skin and mucosa (Langerhans cells). This article reports a case of multisystemic Langerhans cell histiocytosis diagnosed by autopsy of a four-day newborn with confirmation by immunohistochemistry and secondary systemic infection associated.
Key words:
Langerhans-cell histiocytosis; Langerhans cells; sepsis
