The authors report the case of a 52 year-old woman that presented macroscopic hematuria and pelvic pain. Ultrasound examination was performed, which showed an expansive mass in the bladder floor. A cystoscopy confirmed the presence of this lesion and a biopsy was carried out. Histological analysis showed a small cell neoplasm. The immunohistochemical analysis was required to establish diagnosis. This analysis revealed positivity for EWS-FLI1, CD99 and S-100. The conclusive diagnosis was primitive neuroectodermal tumor. The patient was treated with chemotherapy. After a seven month follow-up period, the patient is disease-free.
Primitive neuroectodermal tumor; Urinary bladder