The primary forms of pulmonary vasculitis are characterized by an inflammatory process in the pulmonary vessel walls, leading to pulmonary ischemia and hemorrhage and the consequent clinical and radiological manifestations. These forms of vasculitis are accompanied by symptoms involving the skin, peripheral nerves, kidneys, sinuses, eyes, ears and gastrointestinal tract, as well as the cardiac and central nervous systems. The diagnosis is made through analysis of the clinical, radiological and pathological data. When treatment with corticosteroids and immunosuppressive therapy is initiated early, remission rates are high.
Vasculitis; Vasculitis; Lung diseases; Lung diseases; Wegener's granulomatosis; Churg-Strauss syndrome; Diagnosis, differential; Antibodies, antineutrophil cytoplasmic; Adrenal córtex hormones; Immunosuppressive agents; Skin manifestations; Ocular manifestations; Neurological manifestations
