This article reports a case of a female child, nine-years old, with a history of proptosis and progressive decrease of visual acuity. At ophthalmologic exam presented: best corrected visual acuity 20/20 on the right eye and light perception on the left eye; biomicroscopic exam was normal, weakness of left superior rectus and left inferior oblique muscle, exotropia and hypotropia to the left. At indirect ophthalmoscopy exam, fundus was normal on the right eye and had left optic disc with edema. computerized tomography showed a hiperdense tumor, fusiform shape in the optic pathway, suggesting optic nerve glioma. At physical exam, it was verified " café-au-lait" spots in the thorax and armpits and axillary freckles in the region, filling criteria to neurofibromatosis type I ( Von Recklinghausen´s disease).
Optic nerve glioma; Neurofibromatosis 1; Visual acuity; Case reports
