Branch retinal artery occlusion in Susac's syndrome

Oclusão de ramo arterial da retina na Síndrome de Susac

Susac's syndrome is a rare disease attribuited to a microangiopathy involving the arterioles of the cochlea, retina and brain. Encefalopathy, hearing loss, and visual deficits are the hallmarks of the disease. Visual loss is due to multiple, recurrent branch arterial retinal occlusions. We report a case of a 20-year-old women with Susac syndrome presented with peripheral vestibular syndrome, hearing loss, ataxia, vertigo, and vision loss due occlusion of the retinal branch artery.

Vasculitis; Cerebrovascular disorders; Retinal artery occlusion; Hearing loss; Susac’s Syndrome