Neurofibrossarcoma associado a neurofibromatose

Neurofibrosarcoma associated to neurofibromatosis

Neurofibromatosis; Von Recklinghausen; Pelvic neurofibrosarcoma

RELATOS DE CASO

Neurofibrossarcoma associado a neurofibromatose

Neurofibrosarcoma associated to neurofibromatosis

Alcino Lázaro da Silva, TCBC. MG^I; Venício do Amaral Quirino^II

^IProfessor Titular de Cirurgia do Aparelho Digestivo

^IIResidente de Cirurgia

^{Endereço para correspondência}

ABSTRACT

The clinical and pathological aspects of neurofibromatosis are summarized and an updated pathogeny of the tumor is made. The malignancy of the NFS senns to be linled to the NF - 1 gene mutations, with loss of the suppressor gene in the chromosone 17 pl. The surgical treatment is always useful because it lowers the pressure and relieves the patient.

Key words: Neurofibromatosis; Von Recklinghausen; Pelvic neurofibrosarcoma.

Texto completo disponível apenas em PDF.

Full text available only in PDF format.

Recebido em 16/6/97

Aceito para publicação em 22/6/98

Trabalho do Departamento de Cirurgia da Faculdade de Medicina Federal de Minas Gerais.

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• 2. Menom AG, Anderson KM, Riccardi VM, et al. Chromosome 17p deletions and p53 gene mutations associated with the formation of malignant neurofibrosarcoma in Von Recklinghausen neurofibromatosis. Proc Natl Acad Sci USA 1990; 87(14); 5435-9.
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• 5. Chanoki M, Ishii M, Fukai K, et al. Immunohistochemical localization of type I, III, IV, V and VI collagens and laminin in neurofibrorna and neurofibrosarcoma. Am J Dermatopathol 1991;13(4);365-73.

Endereço para correspondência:

Dr. Alcino Lázaro da Silva

Rua Guaratinga, 151 - Sion

30315-430 - Belo Horizonte - MG

Datas de Publicação

• Publicação nesta coleção
  23 Jul 2010
• Data do Fascículo
  Ago 1998

Histórico

• Aceito
  22 Jun 1998
• Recebido
  16 Jun 1997