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Arquivos Brasileiros de Oftalmologia
On-line version ISSN 1678-2925
COSTANZI, Márcio Alberto and CRUZ, Antonio Augusto Velasco e. McCune Albright syndrome - diffuse orbital involvement due to fibrous dysplasia: a case report. Arq. Bras. Oftalmol. [online]. 2007, vol.70, n.6, pp. 1021-1023. ISSN 1678-2925. http://dx.doi.org/10.1590/S0004-27492007000600026.
Fibrous dysplasia is a benign, slowly progressive bone disorder, in which normal bone is replaced by fibrous tissue. It is called McCune Albright syndrome when associated with skin hyperpigmentation and endocrinological disorders. We report a rare case of McCune Albright syndrome in a boy, who presented bilateral and diffuse involvement of orbits but few external craniofacial distortions.
Keywords : Fibrous dysplasia, polyostotic [diagnosis]; Orbital diseases; Craniofacial abnormalities; Facial bones [abnormalities].