Abstract

COSTANZI, Márcio Alberto  and  CRUZ, Antonio Augusto Velasco e. McCune Albright syndrome - diffuse orbital involvement due to fibrous dysplasia: a case report. Arq. Bras. Oftalmol. [online]. 2007, vol.70, n.6, pp. 1021-1023. ISSN 0004-2749.  http://dx.doi.org/10.1590/S0004-27492007000600026.

Fibrous dysplasia is a benign, slowly progressive bone disorder, in which normal bone is replaced by fibrous tissue. It is called McCune Albright syndrome when associated with skin hyperpigmentation and endocrinological disorders. We report a rare case of McCune Albright syndrome in a boy, who presented bilateral and diffuse involvement of orbits but few external craniofacial distortions.

Keywords : Fibrous dysplasia, polyostotic [diagnosis]; Orbital diseases; Craniofacial abnormalities; Facial bones [abnormalities].