SciELO - Scientific Electronic Library Online

 
vol.80 issue6Macrophage activation syndrome associated with systemic juvenile idiopathic arthritis author indexsubject indexarticles search
Home Pagealphabetic serial listing  

Jornal de Pediatria

Print version ISSN 0021-7557

Abstract

FERNANDEZ, Pedro M.; LUCIO, Luiz A.G.  and  POLLACHI, Fabíola. Esophageal achalasia of unknown etiology in children. J. Pediatr. (Rio J.) [online]. 2004, vol.80, n.6, pp. 523-526. ISSN 0021-7557.  http://dx.doi.org/10.1590/S0021-75572004000800016.

OBJECTIVE: To report a case of a 9-year-old female presented with esophageal achalasia and approached with surgery. The authors discuss the treatment and make a literature review on the topic. DESCRIPTION: Childhood esophageal achalasia is an unusual disease, often with unknown etiology. The main symptoms are esophageal vomits, dysphagia and weight loss. The diagnosis can be made by esophagogram and endoscopy, but the main examination is the esophageal manometry. Even though the surgical approach is a well-established therapy, some alternative treatments have been used, such as the endoscopy balloon dilatation and the use of botulinum toxin. COMMENTS: Esophageal achalasia is a rare disease in childhood, with unknown etiology. The presentation may be confused with gastroeshophageal reflux, sometimes causing a diagnosis delay. The surgical approach, as well as an antireflux procedure, is the treatment of choice.

Keywords : Dilated esophagus; gastroeshophageal reflux; childhood; esophagomyotomy; pneumatic balloon dilatation; botulinum toxin.

        · abstract in Portuguese     · text in English | Portuguese     · pdf in English | Portuguese