SciELO - Scientific Electronic Library Online

vol.56 issue6Lumbar plexopathy after abdominal hysterectomy: case reportUse of the lateral approach for laryngeal mask insertion during awake craniotomy: case report author indexsubject indexarticles search
Home Pagealphabetic serial listing  

Services on Demand




Related links


Revista Brasileira de Anestesiologia

Print version ISSN 0034-7094On-line version ISSN 1806-907X


ARAUJO, Fabiano Souza et al. Anesthesia in a patient with Steinert disease: case report. Rev. Bras. Anestesiol. [online]. 2006, vol.56, n.6, pp.649-653. ISSN 0034-7094.

BACKGROUND AND OBJECTIVES: Steinert disease is the most common muscular dystrophy of the adult. Due to its multisystem characteristic, the perioperative management of these patients is a challenge to the anesthesiologist. The aim of this report was to present a case of hemorrhoidectomy in a patient with muscular dystrophy and to discuss the several anesthetic implications involved. CASE REPORT: A man patient, 58 years old, with Steinert disease, who underwent hemorrhoidectomy. Subaracnoid block with hyperbaric bupivacaine (saddle block with puncture at L3-L4 with 0.5% bupivacaine [5 mg]) associated with sedation with propofol (1 µg.mL-1 target using a target-controlled infusion pump). Dypirone (1.5 g) and local infiltration with 0.5% ropivacaine (150 mg) were used for the postoperative analgesia. Intraoperatively, the patient developed myotonic crisis (10 minutes after being placed on the litothomy position) that was controlled by sedation (the target concentration was increased to 1.5 µg.mL-1 and given a bolus of 40 mg). The patient remained stable and was discharged the following day. CONCLUSIONS: The knowledge about the disease and the proper anesthetic planning are extremely important when managing patients with Steinert disease.

Keywords : ANESTHETIC TECHNIQUES, Regional [spinal block]; DISEASE, Neurologic [Steinert disease].

        · abstract in Portuguese | Spanish     · text in English | Portuguese     · English ( pdf epdf ) | Portuguese ( pdf epdf )


Creative Commons License All the contents of this journal, except where otherwise noted, is licensed under a Creative Commons Attribution License