Acalvaria is a rare congenital malformation of unknown pathogenesis characterized by the absence of the flat bones of the cranial vault, dura mater and associated muscles, while the central nervous system is usually preserved. The most accepted physiopathogenic theory suggests the presence of a postneurulation defect with normal placement the embryonic ectoderm. The present report describes neonatal imaging findings of primary acalvaria.
Primary acalvaria; Skull defect; Congenital malformation
