Revista Brasileira de Coloproctologia
Print version ISSN 0101-9880
FERNANDES, Cristiane Koizimi Martos et al. The Tailgut Cyst is na embryological remnant of the retrorectal (Presacral) space that can be a part of the currarino syndrome. Rev bras. colo-proctol. [online]. 2007, vol.27, n.4, pp. 446-451. ISSN 0101-9880. http://dx.doi.org/10.1590/S0101-98802007000400013.
The Tailgut Cyst is an embryological remnant of the hindgut that can be a part of the Currarino Syndrome. Report of a case: A 43-year-old woman with lombalgy, urine retain and presacral mass. Preceding history of ectopic anus, constipation associated with congenital megacolon. Imaging exams indicate retrorectal cyst that compresses the sacral region, receding the pelvic structure forward and congenital sacral deformity. A block resection of the retrorectal, rectal, uterus and sacrum lesion was carried out in a S2 level. Anatomo-pathologic indicate tailgut cyst. The patient is characterized as carrying the Currarino Syndrome. Discussion: The syndrome is characterized by the malformation of the anorectal, sacral abnormalties and retrorectal mass. It has connection with a gene mutation of the HLXB9. The Tailgut Cyst is an embryological remnant of the hindgut, more common in young adult women (75-90%). The tailgut cyst related to the Currarino Syndrome is an uncommom lesion. Most patients are asymptomatic, however, they may present anorectal, perineo and sacrum symptoms. Imaging exams are useful for diagnostic definition and surgery programming. The complete surgery excision is recommended due to the risk of reestablishment, malignant degeneration and chronic infection, even in asymptomatic patients. The prognosis is uncertain.
Keywords : Tailgut Cyst; Retroretal Cyst; Presacral Cyst; Currarino Syndrome.