Anais Brasileiros de Dermatologia
On-line version ISSN 1806-4841
MARTINS, Gladys Aires; ABDALA, Wadad Gonzaga and ANDRADE, Daniela Velozo de. Scleromyxedema with associated cardiomyopathy. An. Bras. Dermatol. [online]. 2004, vol.79, n.5, pp. 561-566. ISSN 1806-4841. http://dx.doi.org/10.1590/S0365-05962004000500006.
We report a case of scleromyxedema with skin lesions in association with myopathy, esophageal dysfunction and paraproteinemia. During the disease course, the patient developed symptoms of cardiac failure related to a cardiomyopathy, a condition that has been described in up to 10% of patients with scleromyxedema. The clinical, etiologic and therapeutic aspects are discussed in this paper.
Keywords : heart failure [congestive]; myositis; mucinoses; paraproteinemias.