Anais Brasileiros de Dermatologia
Print version ISSN 0365-0596
On-line version ISSN 1806-4841
BADZIAK, Daniela et al. Acquired perforating dermatosis associated with hepatic failure in a liver-transplanted patient. An. Bras. Dermatol. [online]. 2007, vol.82, n.1, pp.53-56. ISSN 0365-0596. http://dx.doi.org/10.1590/S0365-05962007000100007.
Acquired perforating dermatosis is characterized by transepithelial elimination of degenerated dermal substances. It occurs in many conditions, such as: diabetes mellitus, chronic renal failure and sclerosing cholangitis. This article describes a 17-year-old Caucasian female with type I glucogenosis and acquired perforating dermatosis due to chronic hepatic failure caused by hepatic complication of liver transplant.
Keywords : Cholestasis; Folliculitis; Glycogen storage disease type I; Keratin; Liver failure; Liver transplantation; Pruritus.