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Anais Brasileiros de Dermatologia
versão impressa ISSN 0365-0596versão On-line ISSN 1806-4841
Resumo
BEDRIKOW, Roberta Buense; FARIAS, Débora Cadore de; MAIA, Marcus e MULLER, Helena. Do you know this syndrome?. An. Bras. Dermatol. [online]. 2007, vol.82, n.5, pp.477-479. ISSN 1806-4841. https://doi.org/10.1590/S0365-05962007000500012.
Pachydermoperiostosis is a rare autosomal dominant genodermatosis characterized by bone and cutaneous involvement, even though its prevalence and incidence are ignored. It occurs predominantly in men, which present a more serious clinical presentation. We report a case of a 60-year-old man with this disease.
Palavras-chave : Facial dermatoses; Hyperostosis; Osteoarthropathy, primary hypertrophic.