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Anais Brasileiros de Dermatologia

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Abstract

CUMMING, Moema Mignac et al. Febrile ulceronecrotic Mucha-Habermann disease with exuberant mucosal involvement: case report. An. Bras. Dermatol. [online]. 2009, vol.84, n.6, pp. 655-658. ISSN 0365-0596.  http://dx.doi.org/10.1590/S0365-05962009000600012.

Pityriasis lichenoides is a rare idiopathic cutaneous disorder, with a clinical-histopathological spectrum comprising the acute varioliform form (Mucha-Habermann's disease), its febrile ulceronecrotic variant, and its chronic form. Systemic manifestations may occur in the febrile ulceronecrotic variant, with reports of adult mortality. The case of a young male patient with clinical and histopathological diagnosis of Mucha-Habermann’s disease, febrile ulceronecrotic variant, with severe mucosal involvement - an occasional incidence even in the most severe forms of pityriasis lichenoides - is presented. In addition to the atypical clinical aspect, an excellent therapeutic result is shown with the association of prednisone and methotrexate.

Keywords : Methotrexate; Pityriasis lichenoides; Prednisone.

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