Anais Brasileiros de Dermatologia
On-line version ISSN 1806-4841
CUMMING, Moema Mignac et al. Febrile ulceronecrotic Mucha-Habermann disease with exuberant mucosal involvement: case report. An. Bras. Dermatol. [online]. 2009, vol.84, n.6, pp.655-658. ISSN 1806-4841. http://dx.doi.org/10.1590/S0365-05962009000600012.
Pityriasis lichenoides is a rare idiopathic cutaneous disorder, with a clinical-histopathological spectrum comprising the acute varioliform form (Mucha-Habermann's disease), its febrile ulceronecrotic variant, and its chronic form. Systemic manifestations may occur in the febrile ulceronecrotic variant, with reports of adult mortality. The case of a young male patient with clinical and histopathological diagnosis of Mucha-Habermann’s disease, febrile ulceronecrotic variant, with severe mucosal involvement - an occasional incidence even in the most severe forms of pityriasis lichenoides - is presented. In addition to the atypical clinical aspect, an excellent therapeutic result is shown with the association of prednisone and methotrexate.
Keywords : Methotrexate; Pityriasis lichenoides; Prednisone.