Anais Brasileiros de Dermatologia
Print version ISSN 0365-0596
BERBERT, Alceu L. C. V. et al. Keratosis follicularis spinulosa decalvans: case report. An. Bras. Dermatol. [online]. 2010, vol.85, n.4, pp. 537-540. ISSN 0365-0596. http://dx.doi.org/10.1590/S0365-05962010000400017.
Keratosis follicularis spinulosa decalvans is a rare disease, with genetic transmission either X-linked or sporadic, characterized by follicular hyperkeratosis and cicatricial alopecia. The disease usually begins in early childhood exacerbating throughout adolescence. The therapies are somewhat effective, with frustrating treatment when there are changes which are predominantly cicatricial. It is reported a case of child with intense cicatricial alopecia, with precocious changes (already present at birth) that rapidly evolved to diffuse cicatricial alopecia on the scalp, which has limited the treatment, with disappointing results.
Keywords : Hair follicle; Keratosis; Scalp dermatoses; Skin and connective tissue diseases.