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Anais Brasileiros de Dermatologia
On-line version ISSN 1806-4841
NASSIF, Priscila Wolf et al. Febrile ulceronecrotic Mucha-Habermann disease in adult patient successfully treated with systemic corticosteroid. An. Bras. Dermatol. [online]. 2010, vol.85, n.6, pp.891-894. ISSN 1806-4841. http://dx.doi.org/10.1590/S0365-05962010000600018.
The Febrile Ulceronecrotic Mucha-Habermann (FUMHD) disease is a rare variant of pityriasis lichenoides et varioliformis acuta (PLEVA). Its etiology still remains unknown and it is characterized by a sudden onset of ulceronecrotic skin lesions associated with systemic symptons. It is reported here the case of a male patient with a sudden and acute evolution of macules and papules, ulceronecrotic and vesicle-bullous lesions associated with systemic symptons. The patient was treated with prednisone 0,5 mg/kg/day with a dramatic response. The FUMHD is a severe variant of PLEVA and its diagnosis is clinical and histopathological. Many treatments such as methotrexate, corticosteroids and PUVA have been described .However, none of them has been settled.
Keywords : Adrenal cortex hormones; Pityriasis lichenoides; Vasculitis.