SciELO - Scientific Electronic Library Online

 
vol.85 issue6Dermatophytosis caused by Tricophyton rubrum as an opportunistic infection in patients with Cushing diseaseMilia en plaque author indexsubject indexarticles search
Home Pagealphabetic serial listing  

Anais Brasileiros de Dermatologia

Print version ISSN 0365-0596

Abstract

NASSIF, Priscila Wolf et al. Febrile ulceronecrotic Mucha-Habermann disease in adult patient successfully treated with systemic corticosteroid. An. Bras. Dermatol. [online]. 2010, vol.85, n.6, pp. 891-894. ISSN 0365-0596.  http://dx.doi.org/10.1590/S0365-05962010000600018.

The Febrile Ulceronecrotic Mucha-Habermann (FUMHD) disease is a rare variant of pityriasis lichenoides et varioliformis acuta (PLEVA). Its etiology still remains unknown and it is characterized by a sudden onset of ulceronecrotic skin lesions associated with systemic symptons. It is reported here the case of a male patient with a sudden and acute evolution of macules and papules, ulceronecrotic and vesicle-bullous lesions associated with systemic symptons. The patient was treated with prednisone 0,5 mg/kg/day with a dramatic response. The FUMHD is a severe variant of PLEVA and its diagnosis is clinical and histopathological. Many treatments such as methotrexate, corticosteroids and PUVA have been described .However, none of them has been settled.

Keywords : Adrenal cortex hormones; Pityriasis lichenoides; Vasculitis.

        · abstract in Portuguese     · text in English | Portuguese     · pdf in English | Portuguese