Anais Brasileiros de Dermatologia
Print version ISSN 0365-0596
ALBUQUERQUE, Lígia Guedes Morais de et al. Primary erythromelalgia: case report. An. Bras. Dermatol. [online]. 2011, vol.86, n.1, pp. 131-134. ISSN 0365-0596. http://dx.doi.org/10.1590/S0365-05962011000100019.
Erythromelalgia is a rare clinical syndrome characterized by heat, redness and intermittent pain in the extremities, being most frequent the bilateral development in the lower extremities. Local cooling brings relief to symptoms, while heating, physical exercises and use of stockings/socks intensify the discomfort. This condition can be primary or idiopathic or secondary to haematological disorders and vascular inflammatory and degenerative diseases. It is reported the case of an eighteen-year-old male who presented, at the early age of two, development of the symptoms of erythema ,heat and pain followed by desquamation of hands and feet, in outbreaks, with intervals 4 to 5 years long between the crises.
Keywords : Erythema; Erythromelalgia; Hot temperature; Pain.