Anais Brasileiros de Dermatologia
Print version ISSN 0365-0596
GUERINI, Marina Besen et al. Pachydermoperiostosis: the complete form of the syndrome. An. Bras. Dermatol. [online]. 2011, vol.86, n.3, pp. 582-584. ISSN 0365-0596. http://dx.doi.org/10.1590/S0365-05962011000300027.
Pachydermoperiostosis is a rare genodermatosis with various clinical presentations that include pachydermia (thickening of the skin), finger clubbing and periostitis. Its pathogenesis is uncertain and the condition affects mainly men. This report describes the case of a patient with typical, exuberant skin manifestations and classic radiological findings of this syndrome in its complete form
Keywords : Hyperostosis; Osteoarthropathy, primary hypertrophic; Skin diseases.