Abstract

BAETA, Isabela Guimarães Ribeiro; PEREIRA, Ana Carolina Figueiredo; GUEDES, Antônio Carlos Martins  and  PEREIRA, Luciana Baptista. Do you know this syndrome?. An. Bras. Dermatol. [online]. 2011, vol.86, n.3, pp. 605-607. ISSN 0365-0596.  http://dx.doi.org/10.1590/S0365-05962011000300036.

Keratosis linearis with ichthyosis congenita and sclerosing keratoderma (KLICK) syndrome is a rare autosomal recessive skin disorder characterized by the association of diffuse, transgressive palmoplantar keratoderma with sclerodactyly, linear hyperkeratotic plaques generally located in flexures, and congenital ichthyosis. The patient is physically and mentally healthy and has no history of any problems related to teeth, nails, hair or mucous membranes. Treatment is based on the use of topical keratolytics and oral retinoids

Keywords : Ichthyosis; Keratoderma, palmoplantar; Keratosis.