Anais Brasileiros de Dermatologia
Print version ISSN 0365-0596
MARTINS FILHO, Paulo Ricardo Saquete et al. Familial case of oral white sponge nevus: a rare hereditary condition. An. Bras. Dermatol. [online]. 2011, vol.86, n.4, suppl.1, pp. 39-41. ISSN 0365-0596. http://dx.doi.org/10.1590/S0365-05962011000700009.
White sponge nevus (WSN) is an autosomal dominant skin disorder characterized by white, corrugated and diffuse plaques mainly affecting the oral mucosa. The condition has a high penetrance and variable expressivity, but familial reports are uncommon. This report presents a familial case of WSN in which two sisters are affected by the disorder
Keywords : Leukokeratosis; Hereditary mucosal; Oral mucosa; Nevus.