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Anais Brasileiros de Dermatologia

Print version ISSN 0365-0596On-line version ISSN 1806-4841


VILLARREAL, Delky Johanna Villarreal  and  LEAL, Fabiano. Phacomatosis pigmentovascularis of cesioflammea type. An. Bras. Dermatol. [online]. 2016, vol.91, n.5, suppl.1, pp.54-56. ISSN 0365-0596.

Phacomatosis pigmentovascularis is a rare syndrome, defined as the simultaneous presence of vascular nevus and melanocytic nevus in the same patient. We report the case of a 53-year-old woman presented with dermal melanosis and extensive vascular nevus, which match the typical manifestations of phakomatosis pigmetovascularis of cesioflammea type, according to Happle's classification. The rare occurrence of this genodermatosis and the clinical exuberance of the skin lesions motivated this case report.

Keywords : Melanocytes; Nevus; Nevus of Ota; Port-wine stain; Skin abnormalities; Skin pigmentation.

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