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Adult linear IgA bullous dermatosis: report of three cases* * Work conducted at the Department of Dermatology, Universidade Federal de São Paulo (Unifesp), São Paulo (SP), Brasil.

Abstract:

Linear immunoglobulin A bullous dermatosis is a rare autoimmune disease that usually has an excellent prognosis in childhood; however, its control is more difficult in adults. It presents heterogeneous clinical manifestations and is frequently confused with other bullous diseases such as bullous pemphigoid and Duhring’s dermatitis herpetiformis. Dermatologists’ awareness of this disease contributes to early diagnosis and appropriate treatment. We thus report three cases of linear immunoglobulin A dermatosis in adults.

Keywords:
Immunoglobulin A; Linear IgA bullous dermatosis; Skin diseases, vesiculobullous

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