Resumo

TANSINI, Paula Baldissera; BOFF, Ana Letícia; WEBER, Magda Blessmann  e  BONAMIGO, Renan Rangel. Familial “benign” pemphigus? Erythroderma and fatal outcome^,. An. Bras. Dermatol. [online]. 2020, vol.95, n.1, pp.75-77.  Epub 30-Mar-2020. ISSN 1806-4841.  http://dx.doi.org/10.1016/j.abd.2019.02.006.

Hailey-Hailey disease, or familial benign pemphigus, is a rare bullous genodermatosis that usually presents with flaccid blisters, erosions, and maceration limited to flexural areas, resulting in increased morbidity and reduced quality of life for affected patients. The authors report an unusual case of generalized Hailey-Hailey disease with erythroderma and fatal outcome.

Palavras-chave : Pemphigus, benign familial; Dermatitis, exfoliative; Skin diseases, vesiculobullous.

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