Revista Brasileira de Reumatologia
On-line version ISSN 1809-4570
PARCHEN, Carlos Frederico Rodrigues et al. Pulmonary arterial hypertension and cerebrovascular disease in patient with Takayasu Arteritis. Rev. Bras. Reumatol. [online]. 2006, vol.46, n.6, pp. 428-431. ISSN 1809-4570. http://dx.doi.org/10.1590/S0482-50042006000600013.
Takayasu arteritis (TA) is a rare illness characterized by vasculitis of great vessels, mainly of aorta and its branches. The vascular inflammation leads to irregularities of the vessel wall causing stenosis and aneurysms. The pulmonary artery (PA) involvement is frequent in TA. Despite this, the development of pulmonary arterial hypertension is less common, modifying the treatment and the prognosis of the patients. We describe a case of a patient with TA with multiple stenosis in pulmonary arteries, pulmonary arterial hypertension and cerebrovascular disease, as well as review of the literature on the subject.
Keywords : vasculitis; Takayasu arteritis; pulmonary hypertension.