SciELO - Scientific Electronic Library Online

vol.13 issue4Identification of chewing and swallowing changes in individuals submitted to partial glossectomySound localization and lateralization in individuals with visual deficiency author indexsubject indexarticles search
Home Pagealphabetic serial listing  

Services on Demand




Related links


Revista da Sociedade Brasileira de Fonoaudiologia

On-line version ISSN 1982-0232


LINS, Lorene Lemos et al. Audiologic findings in individuals with Steinert's myotonic dystrophy. Rev. soc. bras. fonoaudiol. [online]. 2008, vol.13, n.4, pp.344-351. ISSN 1982-0232.

PURPOSE: To identify the main hearing disorders in individuals with Steinert's myotonic dystrophy. METHODS: Five individuals were submitted to tonal and vocal audiometry, acoustic impedance tests, examination of Eustaquian tube function, acoustic reflex investigation, and acoustic reflex decay. They also answered two questionnaires: a) Performance of auditory function; b) Psycho-acoustic-social investigation. RESULTS: The study showed that 60% of the sample presented normal hearing thresholds, 10% had conductive hearing loss and 30% had hearing loss in high frequencies. Concerning acoustic reflexes, it was observed that 30% of the subjects presented deficits at 0.5 and 1 kHz and 40% at 2 and 4 kHz. Acoustic reflex decay was observed in 10% of the sample at 0,5 and 1 kHz. CONCLUSION: The study showed that the typical auditory profile of high-frequencies hearing loss was observed in 30% of the sample.

Keywords : Myotonic dystrophy [physiopathology]; Myotonic dystrophy [complications]; Hearing disorders; Hearing; Acoustic impedance tests; Stapedius; Eustachian tube; Reflex [genetics].

        · abstract in Portuguese     · text in Portuguese     · Portuguese ( pdf )


Creative Commons License All the contents of this journal, except where otherwise noted, is licensed under a Creative Commons Attribution License