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EXTRADURAL SPINAL CORD HEMANGIOBLASTOMA: A CASE REPORT AND LITERATURE REVIEW

HEMANGIOBLASTOMA EXTRADURAL MEDULAR: RELATO DE CASO E REVISÃO DE LITERATURA

HEMANGIOBLASTOMA EXTRADURAL DE LA MÉDULA ESPINAL: INFORME DE UN CASO Y REVISIÓN DE LA LITERATURA

ABSTRACT

Objective:

Hemangioblastoma is a rare vascular sporadically occurring CNS tumor that can be associated with von Hippel-Lindau disease. Hemangioblastomas account for 2-6% of all spinal cord neoplasms and rank third among intramedullary space-occupying lesions.

Methods:

This was the first time in our practice that we had dealt with paravertebral hemangioblastoma with the sandglass growth pattern. The world literature describes only 3 case of a tumor with this growth pattern. Surgical and diagnostic aspects of patient treatment are considered.

Results:

During the operation, we adhered to the following stages: localization of the feeding vessel and of the poles of the tumor, surface dissection of the tumor, en bloc resection of the tumor, and hemostasis of the tumor cavity.

Conclusions:

Hemangioblastoma of extradural localization is a very rare pathology. However, when MRI signs characteristic of a vascular lesion are identified, it is necessary to carry out additional examinations, which may include CT perfusion study and, if required, selective angiography. Level of Evidence 5; Case report.

Keywords:
Spinal cord tumor; Hemangioblastoma; Spine; Neurosurgery

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