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Arquivos de Neuro-Psiquiatria

Print version ISSN 0004-282X

Arq. Neuro-Psiquiatr. vol.30 no.2 São Paulo June 1972

http://dx.doi.org/10.1590/S0004-282X1972000200008 

Miopatia ocular descendente

 

Descending ocular myopathy

 

 

Nunjo FinkelI; Antonio R. Vaz RibeiroII; Maria C. Rodrigues SampaioII

IClínica Neurológica do Hospital dos Servidores do Estado (Rio de Janeiro, GB)
IIClínica Neurológica do Hospital dos Servidores do Estado (Rio de Janeiro, GB); Médicos residentes

 

 


RESUMO

São relatados 4 casos de miopatia ocular descendente (MOD) com história familial levantada em três gerações. Biópsia musculares e eletromiografia em um caso confirmaram o caráter miogênico da doença. A MOD nada mais seria do que uma forma clínica especial de distrofia muscular, de início tardio.


SUMMARY

Four cases of the so-called descending ocular myopathy with a family history in three generations are reported. In the first case muscular biopsy and electromyographic studies proved the myogenic nature of the process. Descending ocular myopathy seems to be just a clinical form of muscular distrophy of late onset.


 

 

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Clínica Neurológica — Hospital dos Servidores do Estado — 20000 Rio de Janeiro, GB — Brasil.

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