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Arquivos de Neuro-Psiquiatria

Print version ISSN 0004-282X

Arq. Neuro-Psiquiatr. vol.33 no.2 São Paulo June 1975

http://dx.doi.org/10.1590/S0004-282X1975000200008 

Comprometimento de estruturas encefálicas não hipotalâmicas na moléstia de Hand-Schüller-Christian. Relato de caso e revisão da literatura

 

Involvement of non-hypothalamic encephalic structures in Hand-Schüller-Christian disease. Report of a case and review of the literature

 

 

José Geraldo Camargo LimaI; Ademir Baptista da SilvaII

IDepartamento de Neurologia e Neurocirurgia da Escola Paulista de Medicina: Professor Adjunto
IIDepartamento de Neurologia e Neurocirurgia da Escola Paulista de Medicina: Médico estagiário

 

 


RESUMO

É relatado um caso de moléstia de Hand-Schüller-Christian que, além de elementos da tríade clássica e retração concêntrica do campo visual, apresentava uma síndrome piramidal. A raridade do comprometimento de estruturas encefálicas não hipotalâmicas nessa moléstia é realçada. É enfatizada a ação benéfica da corticoterapia e radioterapia observada no caso.


SUMMARY

A case of Hand-Schüller-Christian disease which presented a pyramidal syndrome besides elements of the classical triad and concentric retraction of the visual field is reported. The rare involvement of non-hypothalamic encephalic strutures in that disease is emphasized together with the favourable effect of corticotherapy and radiotherapy.


 

 

Texto completo disponível apenas em PDF.

Full text available only in PDF format.

 

 

REFERÊNCIAS

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Departamento de Neurologia e Neurocirurgia — Escola Paulista de Medicina — Caixa Postal 5496 — 01000 São Paulo, SP — Brasil.
Trabalho do Departamento de Neurologia e Neurocirurgia da Escola Paulista de Medicina, apresentado no VI Congresso Brasileiro de Neurologia, (Rio de Janeiro-GB, 8-13 julho de 1974)

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