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Arquivos de Neuro-Psiquiatria

Print version ISSN 0004-282X

Arq. Neuro-Psiquiatr. vol.37 no.3 São Paulo Sept. 1979

https://doi.org/10.1590/S0004-282X1979000300008 

Doença de Sturge-Weber atípica associada a angiomatose metamérica: registro de um caso e revisão da literatura

 

Atypical Sturge-Weber disease with metamerical angiomatosis: report of a case and review of the literature

 

 

Rubens N. A. A. ReimãoI; Antonio B. LefèvreII

IMédico Residente. Departamento de Neuropsiquiatria da Faculdade de Medicina da Universidade de São Paulo
IIProfessor Titular de Neurologia Infantil. Departamento de Neuropsiquiatria da Faculdade de Medicina da Universidade de São Paulo

 

 


RESUMO

Um caso, possivelmente o primeiro, de doença de Sturge-Weber associada à hemangioma plano de distribuição metamérica no tronco e membros é descrito clinicamente. Achados radiológicos incluindo exames contrastados e tomografia axial computadorizada são descritos e discutidos. Comenta-se a relação entre os angiomas neurocutâneos.


SUMMARY

Possibly the first case of Sturge-Weber disease associated with metameric limbs and trunk cutaneous hemangioma is reported. Roentnographic findings including contrast studies and computerized axial tomography are presented and discussed. Comments are made upon the relations between neurocutaneous angiomatosis.


 

 

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Trabalho da Clinica Neurológica do Departamento de Neuropsiquiatria da Faculdade de Medicina da Universidade de São Paulo.
Clinica Neurológica - Faculdade de Medicina, Universidade de São Paulo - Caixa Postal 3461 - 01000 São Paulo, SP - Brasil.

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