Doença de Sturge-Weber atípica associada a angiomatose metamérica: registro de um caso e revisão da literatura

Reimão, Rubens N. A. A.; Lefèvre, Antonio B.

doi:10.1590/S0004-282X1979000300008

Resumos

Um caso, possivelmente o primeiro, de doença de Sturge-Weber associada à hemangioma plano de distribuição metamérica no tronco e membros é descrito clinicamente. Achados radiológicos incluindo exames contrastados e tomografia axial computadorizada são descritos e discutidos. Comenta-se a relação entre os angiomas neurocutâneos.

Possibly the first case of Sturge-Weber disease associated with metameric limbs and trunk cutaneous hemangioma is reported. Roentnographic findings including contrast studies and computerized axial tomography are presented and discussed. Comments are made upon the relations between neurocutaneous angiomatosis.

Doença de Sturge-Weber atípica associada a angiomatose metamérica: registro de um caso e revisão da literatura

Atypical Sturge-Weber disease with metamerical angiomatosis: report of a case and review of the literature

Rubens N. A. A. Reimão^I; Antonio B. Lefèvre^II

^IMédico Residente. Departamento de Neuropsiquiatria da Faculdade de Medicina da Universidade de São Paulo

^IIProfessor Titular de Neurologia Infantil. Departamento de Neuropsiquiatria da Faculdade de Medicina da Universidade de São Paulo

RESUMO

Um caso, possivelmente o primeiro, de doença de Sturge-Weber associada à hemangioma plano de distribuição metamérica no tronco e membros é descrito clinicamente. Achados radiológicos incluindo exames contrastados e tomografia axial computadorizada são descritos e discutidos. Comenta-se a relação entre os angiomas neurocutâneos.

SUMMARY

Possibly the first case of Sturge-Weber disease associated with metameric limbs and trunk cutaneous hemangioma is reported. Roentnographic findings including contrast studies and computerized axial tomography are presented and discussed. Comments are made upon the relations between neurocutaneous angiomatosis.

Texto completo disponível apenas em PDF.

Full text available only in PDF format.

Trabalho da Clinica Neurológica do Departamento de Neuropsiquiatria da Faculdade de Medicina da Universidade de São Paulo.

Clinica Neurológica - Faculdade de Medicina, Universidade de São Paulo - Caixa Postal 3461 - 01000 São Paulo, SP - Brasil.

1. ALEXANDER, G. L. - The Sturge-Weber syndrome. In G. W. Bryn & P. J. vinke, editores- Handbook of Clinical Neurology. North Holland Pub. Co., New York, 1972, Vol. 14, pg. 223-239.
2. ALEXANDER, W. - Angioma recemosum des Rückenmarks. zbl Neurol 28:246, 1922.
3. ALEXANDER, G. L. & NORMAN, R. M. - The Sturge-Weber Syndrome. John Wright & Sons Ltd., Bristol. 1960.
4. ANDRE, J. M.; SCHMITT, J. & KISSEL, P. - Classification generate et limites nosologiques des phacomatoses. J. Genet. Hum. Suppl. 23:187, 1975.
5. ARSENIC, C. & CARP, N. - La maladie de Sturge-Weber: observations anatomo-cliniques et histopathologiques. Ann Anat. Path. 12:411. 1967.
6. BERGES, J. & LfiZINE, I. - The imitation of gestures. Clinic in Developmental Medicine, vol. 18 W. Heinemann Medical Books Ltd, London, 1965.
7. GERGSTRAND, L.; OLIVERCRONA, H. & TÜNNIS, W. - Gefftssmissbildungen und Gefassgeschwülste des Gehirns. G. Thieme, Leipsig, 1936.
8. BOLTSHAUSER, E.; WILSON, J. & HO ARE, R. D. - Sturge-Weber syndrome with bilateral intracranial calcification. J. Neurol. Neurosurg. Psychiatry (London) 39:429, 1976.
9. CHAPUT, J. - Enorme angiome lomboabdominal. Bull. Mém. Soc. Chir. Paris 30:444, 1904.
10. COBB, S. - Hemangioma of the spinal cord associated with skin naevi of the same metamere. Ann. Surg. 62:641, 1915.
11. COLLIGNON, J. & CARLIER, G. - Bilateral form of Sturbe-Weber disease with rare abnormality of the venous drainage. Acta Neurol. Belg 74:81, 1974.
12. CRAIG, J. M. - Encephalotrigeminal angiomatosis (Sturge-Weber disease). J. Neuropath. Exp. Neurol. 8:305, 1949.
13. CROSS, G. O. - Subarachnoid cervical angioma with cutaneous hemangioma of oorrespondig metamere: report of a case and review of the literatura. Arch. Neurol. Psychiat. (Chicago) 58:359, 1947.
14. CUSHING, H. & BAILEY, P. - Tumors arising from blood vessels of the brain. Charles C. Thomas, Springfield, Illinois, 1928.
15. DE SÉZE, S.; HURTH, M.; DJINDJIAN, R.; KAHN, M. H.; HUBAULT, A.; DRILL, A. - A propos d' un cas d'angiomatose metamérique cutâneo - vertébro - medulaire, Rev. Rhum. 33:455, 1966.
16. DEUTSCH, J. WEISSENBACHER, G. WICHALM, K.; WOLF, G.; BARSEGAR, B. - Kombination von Sturge-Weber und Klippel-Trenaunay Syndrom. Klin Pftdiat. 188:464, 1976.
17. DEVIC, E. & TOLOT, G. - Uh cas d' angiomsarcome des meninges de la moelle chez un sujet porteur d'angiomes multiples. Rev. Méd. (Paris) 26:255, 1906.
18. DI CHIRO, G. & LINDREN, E. - Radiographic findings in 14 cases of Sturge-Weber syndrome. Acta Radiol. 35:387a, 1951.
19. DOPPMAN, J. L.; WIRTH, F. P. & DI CHIRO, G. - Value of cutaneous angioma in the arteriographic localization of spinal cord arteriovenous malformations, New Eng. J. Med. 281:1440, 1969.
20. FALKINBURG, L. W.; SILVER, M. L.; KAY, M. N. & STOLL, J. - Sturge-Weber-Dimitri disease: report of a case with necropsy. Pediatrics 22:319, 1958.
21. FRACASSO, L. - L'angiomatosi del midollo spinale. Cervello, 23:81, 1947.
22. FURUKAWA, T. et al. - Sturge-Weber and Klippel-Trenaunay syndrome with nevus of Ots and It ^I Arch Derm. 102:640-645, 1970.
23. GILBERT, I. - Angioma venosum racemosum with angiomatous lesions of skin and omentum. Brit. Med. J. 1:468, 1952.
24. GILLY, R.; LAPRAS, C; TOMMASI, M. - Revol. M.; Challanel, M. J. & Clavel, D. - Maladie de Sturge-Weber-Krabbe. Pediatrie 32:45, 1977.
25. GINSBOURG, M. - Contribution à Γ étude des formes vasculairse pathologiques vertebro-medullaires (angiomes vertebraux, epiduraux, intraduraux). These Méd., Paris 1960.
26. GOLDSTEIN, K. & SCHEERER, M. - Abstract and Concrete Behaviour, Psychological Monographs vol. 53, no 2. American Psychological Washington, 1951.
27. GOTTRON, H. A. & SCHNYDER, V. W. - (eds) - Handbuch der Haut und Geschlechtskrankheiten Springer Verlag, Berlin - Heidelberg - New York, 1966, p. 715.
28. GREENWALD, H. M. & KOOTA, J. - Associated facial and intracranial hemangiomas. Amer. J. Dis. Child. 51:868, 1936.
29. HARPER, P. S. - Sturge-Weber syndrome with Klippel-Trenaunay-Weber syndrome. Birth Defects 7:314, 19/1.
30. HEUSER, M. - De l'entite nosologique des angiomatoses neuro-cutanees (Sturge-Weber et Klippel-Trenaunay). Rev. Neurol. (Paris), 124:213, 1971.
31. HURTH, M. - Des anéursmes artério-veineux de la moelle épiniére: considerations anatomo-cliniques et therapeutiques. A propos de 11 cas estudiés par artériographie. These méd. Paris, 1964.
32. HURTH, M.; DJINDJIAN R. & HOUDART, R. - Exérese complete des anéurys-mes arterio-veineux de la moelle épiniére: interêt de 1' angiographie medulaire selective. A propos de 11 cas. Neurochirurgie (Paris) 14:499, 1968.
33. JESSEN, R. T.; THOMPSON, S. & SMIHT, E. B. - Cobb syndrome. Arch Dermatol. 113:1587, 1977.
34. JOHNSTON, L. M. - Epidural hemangioma with compression of the spinal cord. J. Amer. Ass. 110:119, 1938.
35. KALISCHER, S. - Demonstration des Gehirns eines Kindes mit Teleangiectasie der Linksseintigen Gesichts-Kopfhaut und Hirnoberflfiche, Berlin Klin. Wschr. 34: 1059, 1897.
36. KARSHNER, R. G.; RAND, C. W. & REEVES, D. L. - Epidural hemangioma associated with hemangioma of the vertebrae. Arch. Surg. 39:942, 1939.
37. KISSED, P. & DUREUX, J. B. - Cobb syndrome: Cutaneomeningospinal angiomatosis In Bruyn, G. W. & VINKEN, P. J. (eds.) - Handbook of Clinical Neurology. North Holland Pub. Co. New York, 1972. vol. 14, pp 429-445.
38. KLIPPEL, M. & TRENAUNAY, R. - Du naevus variqueux osteo-hypertrophique. Arch. Gén. Méd. 77:641, 1900.
39. KRABBE, K. H. - Desformes bulbo-spinales eventuelles de la maladie de Sturge-Weber. Rev. Neurol. (Paris) 93:199, 1955.
40. KRABBE, K. H. - Facial and meningeal angiomatosis associated with calcifications of the brain cortex (Weber-Dimitri disease). Clinical and anatomopathologic contribution. Arch. Neurol. Psychiat (Chicago) 32:737, 1934.
41. KRAMER, W. - Syndromes of Klippel-Trenaunay and Sttirge-Weber in the same patient. Psychiat. Neurol. Neurochir (Amsterdam) 66:362, 1963.
42. KRAMER, W. - Klippel-Trenaunay Syndrome. In G. W. Bruyn, & P. J. Vinken, editores - Handbook of Clinical Neurology North-Holland Pub. Co., New York, 1972, vol. 14, pag. 390-404.
43. LEPERCHEY, F. - Questions soulevées par lOrigine et le developpment des angiomes cranio-faciaux à la lumière des données embryologiques. Ann. Otolaryngol. Chir. Cervicofac. 90:45, 1973.
44. LHERMITTE, J. & CORNIL, L. - Sur un cas de syringomyelic avec syringobulbie associée à naevi pigmentaires et vasculaires. Rev. Neurol. (Paris) 50:903-906, 1928.
45. LICHTENSTEIN, B. W. - Sturge-Weber-Dimitri syndrome. Arch. Neurol. & Psychiat. (Chicago) 71:291, 1954.
46. LICHTENSTEIN, B. W. & ROSEMBERG, C. - Sturge-Weber Dimitr's disease. J. Neuropath. Exp. Neurol. 6:369, 1947.
47. LOUIS-BAR, D. - Les rapports entre les angiomatoses du type Sturge-Weber et les autres dysplasies (formes de passage). Acta neurol. Belg. 50:680, 1950.
48. LOUIS-BAR, D. - Paraplégie spasmodique avec vaste angiomatose cutanée, Confi-nia Neurol. (Basel) 7:238, 1947.
49. LUND, M. - On Epilepsy in Sturge-Weber's disease. Acta Psychiat. Scand. 24: 569, 1949.
50. MATTOS, J. P. - Sindrome de Klippel-Trenaunay-Parkes-Weber com angiomatose medular. Arq. Neuro-Psiquiat. (Sâo Paulo) 33:278, 1975.
51. MELARAGNO FILHO, R.; ANGHINAH, A.; PAULO R. ARAÚJO, R. - Angiomatose épidurale et cutanée. Rev. Neurol. (Paris) 93:783, 1955.
52. MILLER, S. J. H. - Ophtalmic aspects of Sturge-Weber syndrome. Proc. Roy. Soc. Med. 56:419, 1963.
53. MINCKLER, J. - Pathology of the Nervous System, vol. 2, chap. 96 (1350-1351), chap. 142 (1900-1904) 1971.
54. MORGAN, G. - Pathology of the Sturge-Weber syndrome. Proc. Roy. Soc. Med. 56:422, 1963.
55. NELLHAUS, G.; HABERLAND, C. & HILL, B. J. - Sturge-Weber disease With bilateral intracranial calcifications at birth and unusual pathologic findings. Acta Neurol Scand 43:314, 1967.
56. NEILSEN, J. M.; MARVIN, S. L. & SELETZ, E. - Telangiectasis of skin and spinal cord. Bull. Los Angeles Neurol. 23:97, 1958.
57. PETERMAN, A. F.; HAYLES, A. B.; DECKERTY, M. B. & LOWE, J. G. - Encephalotrigeminal angiomatosis: clinical study of 35 cases. JAMA 167:2169, 1958.
58. PIAGET, J. - La representation de l'espace chez l'enfant. PUF. Paris, 1948.
59. POSER, C. M. TAVERAS, J. M. - Cerebral angiography in encephalotrigeminal angiomatosis. Radiology 68:327, 1957.
60. SCHWANITZ, G.; WISSMULLER, H.; KOCH, G. & RIX - Results of the examination of chromossomes in Sturge-Weber's disease. Folia Clin. Int. (Barcelona) 24:641, 1974.
61. STERNING, W. & JACKIMOWICZ, W. - Cit. por Wyburn-Mason 7i, pag. 196.
62. STREETER, G. L. - The development alterations in the vascular system of the brain of the human embryo. Cont. Embryol. Carneggie, 8:5, 1918.
63. TAKAHASHI, Y.: MARUKO, K.; KOIZUMI, S.; UENO, B. & KUMASHIRO, H. Syndrome of Sturge-Weber and Klippel-Weber in the same patient. Fukushima J. Med. Sci. 20:107, 1974.
64. THIEFFRY, S.; ARTHURIS, M.; FAURÉ, C. & LYON, G. - L'angiomatose de Sturge-Weber. XVIII Cong. Ass. Pediatres Langue Franc. (Geneve) 2:318-348, 1961.
65. TRUPP, M. & SACHS, E. - Vascular tumors of the brain and spinal cord and their treatment. J. Neurosurg. 5:354, 1958.
66. TURNER, O. A. & KERNOHAN - Vascular malformations and vascular tumors involving the spinal cord. Arch. Neurol. Psichiat (Chicago) 46:444, 1941.
67. VAN BOGAERT, L. - Pathologie des angiomatoses. Acta Neurol. Belg 50:525, 1950.
68. VAN BOGAERT - Les dysplasies neuro-ectodermiques congennitales. Rev. Neurol. (Paris) 63:373, 1935.
69. WILLICH, E. VAN; SELLIER, W. & WEIGEL, W., - Die intrakraniellen Verkal-kungen des Kindesalters. Fortschr. Rontgenstr. 116:735, 1972.
70. WOODWARD, M. - The application of Piaget's theory to the training of the subnormal J. Mental Subnormality. 8:3, 1962.
71. WYBURN-MASON, R. - The Vascular Abnormalities and Tumors of the Spinal Cord and its Membranes. A. Kimpton, London, 1943.
72. YAKOVLEV, P. I. & GUTHRIE, R. H. - Congenital ectodermose (neurocutaneous syndromes) in epileptic patients. Arch. Neurol. Psychiat. (Chicago) 26:1145, 1931

Datas de Publicação

Publicação nesta coleção
21 Ago 2012
Data do Fascículo
Set 1979

This work is licensed under a Creative Commons Attribution-NonCommercial 4.0 International License.

[1] 1. ALEXANDER, G. L. - The Sturge-Weber syndrome. In G. W. Bryn & P. J. vinke, editores- Handbook of Clinical Neurology. North Holland Pub. Co., New York, 1972, Vol. 14, pg. 223-239.

[2] 2. ALEXANDER, W. - Angioma recemosum des Rückenmarks. zbl Neurol 28:246, 1922.

[3] 3. ALEXANDER, G. L. & NORMAN, R. M. - The Sturge-Weber Syndrome. John Wright & Sons Ltd., Bristol. 1960.

[4] 4. ANDRE, J. M.; SCHMITT, J. & KISSEL, P. - Classification generate et limites nosologiques des phacomatoses. J. Genet. Hum. Suppl. 23:187, 1975.

[5] 5. ARSENIC, C. & CARP, N. - La maladie de Sturge-Weber: observations anatomo-cliniques et histopathologiques. Ann Anat. Path. 12:411. 1967.

[6] 6. BERGES, J. & LfiZINE, I. - The imitation of gestures. Clinic in Developmental Medicine, vol. 18 W. Heinemann Medical Books Ltd, London, 1965.

[7] 7. GERGSTRAND, L.; OLIVERCRONA, H. & TÜNNIS, W. - Gefftssmissbildungen und Gefassgeschwülste des Gehirns. G. Thieme, Leipsig, 1936.

[8] 8. BOLTSHAUSER, E.; WILSON, J. & HO ARE, R. D. - Sturge-Weber syndrome with bilateral intracranial calcification. J. Neurol. Neurosurg. Psychiatry (London) 39:429, 1976.

[9] 9. CHAPUT, J. - Enorme angiome lomboabdominal. Bull. Mém. Soc. Chir. Paris 30:444, 1904.

[10] 10. COBB, S. - Hemangioma of the spinal cord associated with skin naevi of the same metamere. Ann. Surg. 62:641, 1915.

[11] 11. COLLIGNON, J. & CARLIER, G. - Bilateral form of Sturbe-Weber disease with rare abnormality of the venous drainage. Acta Neurol. Belg 74:81, 1974.

[12] 12. CRAIG, J. M. - Encephalotrigeminal angiomatosis (Sturge-Weber disease). J. Neuropath. Exp. Neurol. 8:305, 1949.

[13] 13. CROSS, G. O. - Subarachnoid cervical angioma with cutaneous hemangioma of oorrespondig metamere: report of a case and review of the literatura. Arch. Neurol. Psychiat. (Chicago) 58:359, 1947.

[14] 14. CUSHING, H. & BAILEY, P. - Tumors arising from blood vessels of the brain. Charles C. Thomas, Springfield, Illinois, 1928.

[15] 15. DE SÉZE, S.; HURTH, M.; DJINDJIAN, R.; KAHN, M. H.; HUBAULT, A.; DRILL, A. - A propos d' un cas d'angiomatose metamérique cutâneo - vertébro - medulaire, Rev. Rhum. 33:455, 1966.

[16] 16. DEUTSCH, J. WEISSENBACHER, G. WICHALM, K.; WOLF, G.; BARSEGAR, B. - Kombination von Sturge-Weber und Klippel-Trenaunay Syndrom. Klin Pftdiat. 188:464, 1976.

[17] 17. DEVIC, E. & TOLOT, G. - Uh cas d' angiomsarcome des meninges de la moelle chez un sujet porteur d'angiomes multiples. Rev. Méd. (Paris) 26:255, 1906.

[18] 18. DI CHIRO, G. & LINDREN, E. - Radiographic findings in 14 cases of Sturge-Weber syndrome. Acta Radiol. 35:387a, 1951.

[19] 19. DOPPMAN, J. L.; WIRTH, F. P. & DI CHIRO, G. - Value of cutaneous angioma in the arteriographic localization of spinal cord arteriovenous malformations, New Eng. J. Med. 281:1440, 1969.

[20] 20. FALKINBURG, L. W.; SILVER, M. L.; KAY, M. N. & STOLL, J. - Sturge-Weber-Dimitri disease: report of a case with necropsy. Pediatrics 22:319, 1958.

[21] 21. FRACASSO, L. - L'angiomatosi del midollo spinale. Cervello, 23:81, 1947.

[22] 22. FURUKAWA, T. et al. - Sturge-Weber and Klippel-Trenaunay syndrome with nevus of Ots and It ^I Arch Derm. 102:640-645, 1970.

[23] 23. GILBERT, I. - Angioma venosum racemosum with angiomatous lesions of skin and omentum. Brit. Med. J. 1:468, 1952.

[24] 24. GILLY, R.; LAPRAS, C; TOMMASI, M. - Revol. M.; Challanel, M. J. & Clavel, D. - Maladie de Sturge-Weber-Krabbe. Pediatrie 32:45, 1977.

[25] 25. GINSBOURG, M. - Contribution à Γ étude des formes vasculairse pathologiques vertebro-medullaires (angiomes vertebraux, epiduraux, intraduraux). These Méd., Paris 1960.

[26] 26. GOLDSTEIN, K. & SCHEERER, M. - Abstract and Concrete Behaviour, Psychological Monographs vol. 53, no 2. American Psychological Washington, 1951.

[27] 27. GOTTRON, H. A. & SCHNYDER, V. W. - (eds) - Handbuch der Haut und Geschlechtskrankheiten Springer Verlag, Berlin - Heidelberg - New York, 1966, p. 715.

[28] 28. GREENWALD, H. M. & KOOTA, J. - Associated facial and intracranial hemangiomas. Amer. J. Dis. Child. 51:868, 1936.

[29] 29. HARPER, P. S. - Sturge-Weber syndrome with Klippel-Trenaunay-Weber syndrome. Birth Defects 7:314, 19/1.

[30] 30. HEUSER, M. - De l'entite nosologique des angiomatoses neuro-cutanees (Sturge-Weber et Klippel-Trenaunay). Rev. Neurol. (Paris), 124:213, 1971.

[31] 31. HURTH, M. - Des anéursmes artério-veineux de la moelle épiniére: considerations anatomo-cliniques et therapeutiques. A propos de 11 cas estudiés par artériographie. These méd. Paris, 1964.

[32] 32. HURTH, M.; DJINDJIAN R. & HOUDART, R. - Exérese complete des anéurys-mes arterio-veineux de la moelle épiniére: interêt de 1' angiographie medulaire selective. A propos de 11 cas. Neurochirurgie (Paris) 14:499, 1968.

[33] 33. JESSEN, R. T.; THOMPSON, S. & SMIHT, E. B. - Cobb syndrome. Arch Dermatol. 113:1587, 1977.

[34] 34. JOHNSTON, L. M. - Epidural hemangioma with compression of the spinal cord. J. Amer. Ass. 110:119, 1938.

[35] 35. KALISCHER, S. - Demonstration des Gehirns eines Kindes mit Teleangiectasie der Linksseintigen Gesichts-Kopfhaut und Hirnoberflfiche, Berlin Klin. Wschr. 34: 1059, 1897.

[36] 36. KARSHNER, R. G.; RAND, C. W. & REEVES, D. L. - Epidural hemangioma associated with hemangioma of the vertebrae. Arch. Surg. 39:942, 1939.

[37] 37. KISSED, P. & DUREUX, J. B. - Cobb syndrome: Cutaneomeningospinal angiomatosis In Bruyn, G. W. & VINKEN, P. J. (eds.) - Handbook of Clinical Neurology. North Holland Pub. Co. New York, 1972. vol. 14, pp 429-445.

[38] 38. KLIPPEL, M. & TRENAUNAY, R. - Du naevus variqueux osteo-hypertrophique. Arch. Gén. Méd. 77:641, 1900.

[39] 39. KRABBE, K. H. - Desformes bulbo-spinales eventuelles de la maladie de Sturge-Weber. Rev. Neurol. (Paris) 93:199, 1955.

[40] 40. KRABBE, K. H. - Facial and meningeal angiomatosis associated with calcifications of the brain cortex (Weber-Dimitri disease). Clinical and anatomopathologic contribution. Arch. Neurol. Psychiat (Chicago) 32:737, 1934.

[41] 41. KRAMER, W. - Syndromes of Klippel-Trenaunay and Sttirge-Weber in the same patient. Psychiat. Neurol. Neurochir (Amsterdam) 66:362, 1963.

[42] 42. KRAMER, W. - Klippel-Trenaunay Syndrome. In G. W. Bruyn, & P. J. Vinken, editores - Handbook of Clinical Neurology North-Holland Pub. Co., New York, 1972, vol. 14, pag. 390-404.

[43] 43. LEPERCHEY, F. - Questions soulevées par lOrigine et le developpment des angiomes cranio-faciaux à la lumière des données embryologiques. Ann. Otolaryngol. Chir. Cervicofac. 90:45, 1973.

[44] 44. LHERMITTE, J. & CORNIL, L. - Sur un cas de syringomyelic avec syringobulbie associée à naevi pigmentaires et vasculaires. Rev. Neurol. (Paris) 50:903-906, 1928.

[45] 45. LICHTENSTEIN, B. W. - Sturge-Weber-Dimitri syndrome. Arch. Neurol. & Psychiat. (Chicago) 71:291, 1954.

[46] 46. LICHTENSTEIN, B. W. & ROSEMBERG, C. - Sturge-Weber Dimitr's disease. J. Neuropath. Exp. Neurol. 6:369, 1947.

[47] 47. LOUIS-BAR, D. - Les rapports entre les angiomatoses du type Sturge-Weber et les autres dysplasies (formes de passage). Acta neurol. Belg. 50:680, 1950.

[48] 48. LOUIS-BAR, D. - Paraplégie spasmodique avec vaste angiomatose cutanée, Confi-nia Neurol. (Basel) 7:238, 1947.

[49] 49. LUND, M. - On Epilepsy in Sturge-Weber's disease. Acta Psychiat. Scand. 24: 569, 1949.

[50] 50. MATTOS, J. P. - Sindrome de Klippel-Trenaunay-Parkes-Weber com angiomatose medular. Arq. Neuro-Psiquiat. (Sâo Paulo) 33:278, 1975.

[51] 51. MELARAGNO FILHO, R.; ANGHINAH, A.; PAULO R. ARAÚJO, R. - Angiomatose épidurale et cutanée. Rev. Neurol. (Paris) 93:783, 1955.

[52] 52. MILLER, S. J. H. - Ophtalmic aspects of Sturge-Weber syndrome. Proc. Roy. Soc. Med. 56:419, 1963.

[53] 53. MINCKLER, J. - Pathology of the Nervous System, vol. 2, chap. 96 (1350-1351), chap. 142 (1900-1904) 1971.

[54] 54. MORGAN, G. - Pathology of the Sturge-Weber syndrome. Proc. Roy. Soc. Med. 56:422, 1963.

[55] 55. NELLHAUS, G.; HABERLAND, C. & HILL, B. J. - Sturge-Weber disease With bilateral intracranial calcifications at birth and unusual pathologic findings. Acta Neurol Scand 43:314, 1967.

[56] 56. NEILSEN, J. M.; MARVIN, S. L. & SELETZ, E. - Telangiectasis of skin and spinal cord. Bull. Los Angeles Neurol. 23:97, 1958.

[57] 57. PETERMAN, A. F.; HAYLES, A. B.; DECKERTY, M. B. & LOWE, J. G. - Encephalotrigeminal angiomatosis: clinical study of 35 cases. JAMA 167:2169, 1958.

[58] 58. PIAGET, J. - La representation de l'espace chez l'enfant. PUF. Paris, 1948.

[59] 59. POSER, C. M. TAVERAS, J. M. - Cerebral angiography in encephalotrigeminal angiomatosis. Radiology 68:327, 1957.

[60] 60. SCHWANITZ, G.; WISSMULLER, H.; KOCH, G. & RIX - Results of the examination of chromossomes in Sturge-Weber's disease. Folia Clin. Int. (Barcelona) 24:641, 1974.

[61] 61. STERNING, W. & JACKIMOWICZ, W. - Cit. por Wyburn-Mason 7i, pag. 196.

[62] 62. STREETER, G. L. - The development alterations in the vascular system of the brain of the human embryo. Cont. Embryol. Carneggie, 8:5, 1918.

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