SciELO - Scientific Electronic Library Online

 
vol.48 issue1Neoplasio lumbosacral radiculopathyRussel's syndrome: diencephalic tumor in a child author indexsubject indexarticles search
Home Pagealphabetic serial listing  

Services on Demand

Journal

Article

Indicators

Related links

Share


Arquivos de Neuro-Psiquiatria

Print version ISSN 0004-282X

Arq. Neuro-Psiquiatr. vol.48 no.1 São Paulo Mar. 1990

http://dx.doi.org/10.1590/S0004-282X1990000100015 

Síndrome de turcot relato de dois casos

 

Turcot's syndrome: report of two cases

 

 

Eduardo A. S. VellutiniI; Felix H. PahlI; Maria José F. VieiraII; Paulo H. P. de AguiarI; Darcy F. VellutiniI; Gilberto M. de AlmeidaI; Angelita Habr-GamaII

IServiços de Neurocirurgia - do Hospital das Clínicas (HC) da Faculdade de Medicina da Universidade de São Paulo (FMUSP) e do Hospital Osvaldo Cruz (São Paulo)
IICirurgia do Aparelho Digestivo - do Hospital das Clínicas (HC) da Faculdade de Medicina da Universidade de São Paulo (FMUSP) e do Hospital Osvaldo Cruz (São Paulo)

 

 


RESUMO

Os autores descrevem dois pacientes com associação de polipose intestinal e tumor do sistema nervoso central (síndrome de Turcot), discutindo aspectos clínicos, genéticos e terapêuticos.


SUMMARY

The authors describe two patients with the association of polyposis-coli and central nervous system tumor (Turcot's syndrome). Clinical, genetic and therapeutic aspects are discussed.


 

 

Texto completo disponível apenas em PDF.

Full text available only in PDF format.

 

 

REFERÊNCIAS

1. Baughman FAJr, List CF, Williams JR, Muldoon JP, Segarra JM, Volkel JS - The glioma-polyposis syndrome. N Engl J Med 281:1345, 1969.         [ Links ]

2. Cohen SB - Familial polyposis coli and its extracolonic manifestations. J Med Genet 19:193, 1982.         [ Links ]

3. Costa OL, Silva DM, Colnago FA, Vieira MS, Musso C - Turcot syndrome: autosomal dominant or recessive transmission? Dis Colon Rectum 30:391, 1987.         [ Links ]

4. França LCM, Sanvito WL - Tumor maligno do sistema nervoso central associado a polipose do colon com degeneração maligna. Arq Neuro-Psiquiat (São Paulo) 27:67, 1969.         [ Links ]

5. Itoh H, Ohsato K, Yao T, lida M, Watanabe H - Turcot's syndrome and its mode of inheritance. GUT 20:414, 1979.         [ Links ]

6. Jagelman DG - Familial polyposis! coli. Surg Clin N Am 63:117, 1983.         [ Links ]

7. McKusick VA - Genetic factors in intestinal polyposis. J Am Med Assoc 182:151, 1962.         [ Links ]

8. Parks TG, Bussey HJR, Lockhart-Mummery HE - Familial polyposis coli associated with extracolonic abnormalities. GUT 11:323, 1970.         [ Links ]

9. Rothman D, Su CP, Kendall AB - Dilemma in a case of Turcot's (glioma-polyposis) syndrome: report of a case. Dis Colon Rectum 18:514, 1975.         [ Links ]

10. Smith WG, Kern BB - The nature of the mutation in familial multiple polyposis. Dis Colon Rectum 16:264, 1973.         [ Links ]

11. Turcot J, Despres JP, Pierre FS - Malignant tumours of the central nervous system associated with familial polyposis of the colon. Dis Colon Rectum 2:465, 1959.         [ Links ]

12. Warde PJ, Canto Al, Cavallante F, Habr-Gama A - Tumor maligno do sistema nervoso central associado a polipose do colon (síndrome de Turcot): apresentação de um caso. Arq Gastroenterol (São Paulo) 13:119, 1976.         [ Links ]

 

 

Dr. Eduardo A. S. Vellutini - Clínica Neurológica, Hospital das Clínicas, FMUSP - Caixa Postal 3461 - 01051 São Paulo SP - Brasil

Creative Commons License All the contents of this journal, except where otherwise noted, is licensed under a Creative Commons Attribution License