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Arquivos de Neuro-Psiquiatria

Print version ISSN 0004-282X

Arq. Neuro-Psiquiatr. vol.49 no.2 São Paulo June 1991 



Creutzfeldt-Jakob disease in Venezuela a case report


Doença de Creutzfeldt-Jakob na Venezuela: registro de caso.



Alejandro J. Caraballo H.

M.D., Servicio de Endemias Rurales, Venezuela.




A case of Creutzfeldt-Jakob disease (CJD) in a 32 year old man is presented. The clinical picture included a rapid progressive dementia associated with ataxia, global aphasia, myoclonus and pyramidal signs, death ocurred after 13 months. The diagnosis of CJD was confirmed by CT and neuropathological studies. This is the first report of CJD occurring in Venezuela.


Registro de caso de doença de Creutzfeldt-Jakob (DCJ) em um paciente com 32 anos de idade. O quadro clínico abrangia demência rapidamente progressiva associada a ataxia, afasia global, miocloniais e sinais piramidais. A morte ocorreu após 13 meses. O diagnóstico foi confirmado por dados dia TC e do estudo neurcpatológico. Este é o primeiro relato de DCJ na Venezuela.



Texto completo disponível apenas em PDF.

Full text available only in PDF format.



Acknowledgement - I thank to Ms Magali de Gómez for her excellent technical assistance.



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Dr. Alejandro J. Caraballo H. - Servicio de Endemias Rurales, Zona XIII de Malariología - Avenida Stadium, Edificio Malariología - San Juan de los Morros, Estado Guárico - Venezuela

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