Creutzfeldt-Jakob disease in Venezuela a case report

Caraballo H., Alejandro J.

doi:10.1590/S0004-282X1991000200019

Abstracts

A case of Creutzfeldt-Jakob disease (CJD) in a 32 year old man is presented. The clinical picture included a rapid progressive dementia associated with ataxia, global aphasia, myoclonus and pyramidal signs, death ocurred after 13 months. The diagnosis of CJD was confirmed by CT and neuropathological studies. This is the first report of CJD occurring in Venezuela.

Registro de caso de doença de Creutzfeldt-Jakob (DCJ) em um paciente com 32 anos de idade. O quadro clínico abrangia demência rapidamente progressiva associada a ataxia, afasia global, miocloniais e sinais piramidais. A morte ocorreu após 13 meses. O diagnóstico foi confirmado por dados dia TC e do estudo neurcpatológico. Este é o primeiro relato de DCJ na Venezuela.

CONTENTS CONTEÚDO

Alejandro J. Caraballo H.

M.D., Servicio de Endemias Rurales, Venezuela.

SUMMARY

A case of Creutzfeldt-Jakob disease (CJD) in a 32 year old man is presented. The clinical picture included a rapid progressive dementia associated with ataxia, global aphasia, myoclonus and pyramidal signs, death ocurred after 13 months. The diagnosis of CJD was confirmed by CT and neuropathological studies. This is the first report of CJD occurring in Venezuela.

RESUMO

Registro de caso de doença de Creutzfeldt-Jakob (DCJ) em um paciente com 32 anos de idade. O quadro clínico abrangia demência rapidamente progressiva associada a ataxia, afasia global, miocloniais e sinais piramidais. A morte ocorreu após 13 meses. O diagnóstico foi confirmado por dados dia TC e do estudo neurcpatológico. Este é o primeiro relato de DCJ na Venezuela.

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Acknowledgement - I thank to Ms Magali de Gómez for her excellent technical assistance.

Dr. Alejandro J. Caraballo H. - Servicio de Endemias Rurales, Zona XIII de Malariología - Avenida Stadium, Edificio Malariología - San Juan de los Morros, Estado Guárico - Venezuela

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