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Tumores intrínsecos benignos da região tectal: considerações a propósito de dois casos

Benign intrinsic tectal tumors: report of two cases

Resumos

O diagnóstico e as condutas terapêuticas nos tumores intrínsecos do tronco encefálico, sofreram grandes transformações com o advento da tomografia computadorizada e da ressonância nuclear magnética. Estes métodos diagnósticos permitiram a identificação de diferentes subgrupos de tumores da região, alguns dos quais passíveis de extirpação cirúrgica, com sobrevida prolongada e eventual cura. Os autores apresentam dois casos de um peculiar grupo de rumores do tectum do mesencéfalo, cujos aspectos tomográficos e manifestações clínicas sugeriam estenose do aqueduto de Sylvius de início tardio. O diagnóstico definitivo foi estabelecido por RNM. Em ambos, os sintomas desapareceram após instalação de derivação ventricular. As características clínico-patológicas e as alternativas terapêuticas deste subgrupo particular de tumores do tronco encefálico são discutidas.

tumores do tronco encefálico; tumores tectais; hidrocefalia; estenose de aqueduto de início tardio


The introduction of computerized tomography and magnetic resonance imaging led to the knowledge that brain stem tumors are not a homogeneous group with regard to their clinical, pathological and biological features. The classical concept of an uniformly poor prognosis has been modified and some subtypes of tumors are amenable to surgical treatment and long-term survival. The authors report two cases of patients with tumors of the tectal region whose symptoms and CT features were consistent with late-onset aqueductal obstruction. In both cases definitive diagnosis was established by MRI and symptoms resolved after ventriculo-peritoneal shunt implantation. The clinic and pathological features and therapeutical alternatives as well, are discussed.

brain stem tumors; tectal tumors; hydrocephalus; late onset aqueduct stenosis


Tumores intrínsecos benignos da região tectal: considerações a propósito de dois casos

Benign intrinsic tectal tumors: report of two cases

J. Francisco Salomão; Renê D. Leibinger; João G. S. Carvalho; Maria Laura B. de Menezes

Serviço de Neurocirurgia Pediátrica, Departamento de Cirurgia, Instituto Fernandes Figueira (MS-Fiocruz), Rio de Janeiro

RESUMO

O diagnóstico e as condutas terapêuticas nos tumores intrínsecos do tronco encefálico, sofreram grandes transformações com o advento da tomografia computadorizada e da ressonância nuclear magnética. Estes métodos diagnósticos permitiram a identificação de diferentes subgrupos de tumores da região, alguns dos quais passíveis de extirpação cirúrgica, com sobrevida prolongada e eventual cura. Os autores apresentam dois casos de um peculiar grupo de rumores do tectum do mesencéfalo, cujos aspectos tomográficos e manifestações clínicas sugeriam estenose do aqueduto de Sylvius de início tardio. O diagnóstico definitivo foi estabelecido por RNM. Em ambos, os sintomas desapareceram após instalação de derivação ventricular. As características clínico-patológicas e as alternativas terapêuticas deste subgrupo particular de tumores do tronco encefálico são discutidas.

Palavras-chave: tumores do tronco encefálico, tumores tectais, hidrocefalia, estenose de aqueduto de início tardio.

SUMMARY

The introduction of computerized tomography and magnetic resonance imaging led to the knowledge that brain stem tumors are not a homogeneous group with regard to their clinical, pathological and biological features. The classical concept of an uniformly poor prognosis has been modified and some subtypes of tumors are amenable to surgical treatment and long-term survival. The authors report two cases of patients with tumors of the tectal region whose symptoms and CT features were consistent with late-onset aqueductal obstruction. In both cases definitive diagnosis was established by MRI and symptoms resolved after ventriculo-peritoneal shunt implantation. The clinic and pathological features and therapeutical alternatives as well, are discussed.

Key words: brain stem tumors, tectal tumors, hydrocephalus, late onset aqueduct stenosis.

Texto completo disponível apenas em PDF.

Full text available only in PDF format.

Aceite: 19-novembro-1993.

Dr. J. Francisco Salomão - Av. N.S. de Copacabana 1018/608 - 22060-130 Rio de Janeiro RJ - Brasil.

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Datas de Publicação

  • Publicação nesta coleção
    19 Jan 2011
  • Data do Fascículo
    Jun 1994
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