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Arquivos de Neuro-Psiquiatria

Print version ISSN 0004-282X

Arq. Neuro-Psiquiatr. vol.52 no.3 São Paulo Sept. 1994 

Síndrome extrapiramidal e hipoparatireoidismo: acerca da identidade da doença de Fahr


Hypoparathyroidism and extrapyramidal syndrome: about the identity of the Fahr disease



Marcelo Gabriel VegaI; Atos Alves de SousaI; Francisco de Lucca JrI; Saulo PurichII; Maria Lucia TenassiII

ISanta Casa de Misericórdia de Belo Horizonte: Serviço de Neurologia e Neurocirurgia
IISanta Casa de Misericórdia de Belo Horizonte: Serviço de Endocrinologia




A presença de calcificações bilaterais dos gânglios da base associadas a manifestações neurológicas foi por muito tempo diagnosticada como doença de Fahr . Apresentamos os casos de dois pacientes com calcificações bilaterais de gânglios da base que apresentavam síndromes extrapiramidais e hipoparatireoidismo. Revimos a literatura pertinente e discutimos a identidade da doença de Fahr e as relações entre calcificações dos gânglios da base, manifestações neurológicas e endócrinas.

Palavras-chave: calcificações, gânglios da base, síndrome extrapiramidal, hipoparatireoidismo, doença de Fahr.


Bilateral calcifications in the basal ganglia associated with neurological manifestations was diagnosed as Fahr disease for a long time. We present the cases of two patients with bilateral calcifications in the basal ganglia who presented hypoparathyroidism and extrapyramidal syndrome. Based on literature review we discuss the identity of Fahr disease and the relationship between calcifications in the basal ganglia and manifestations of endocrine system dysfunctions.

Key words: calcifications, basal ganglia, extrapiramidal syndrome, hypoparathyroidism, Fahr disease



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Aceite: 16-fevereiro-1994.



Dr. Marcelo Gabriel Vega-Rua Ceará 567, 5º andar - 30150-310 Belo Horizonte MG - Brasil.

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