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Arquivos de Neuro-Psiquiatria

versão impressa ISSN 0004-282X

Arq. Neuro-Psiquiatr. vol.52 no.4 São Paulo dez. 1994

http://dx.doi.org/10.1590/S0004-282X1994000400011 

Holoprosencefalia: estudo de seis casos

 

Holoprosencephaly: study of six cases

 

 

Isabel Saraiva LamegoI; Lígia Maria Barbosa-CoutinhoII

IEstudo realizado no Departamento de Patologia da Fundação Faculdade Federal de Ciências Médicas de Porto Alegre (FFFCMPA): Doutoranda da FFFCMPA
IIIEstudo realizado no Departamento de Patologia da Fundação Faculdade Federal de Ciências Médicas de Porto Alegre (FFFCMPA): Professora Titular de Anatomia Patológica da FFFCMPA, Neuropatologista

 

 


RESUMO

Para a realização deste estudo, que tem por objetivo classificar e analisar o aspecto mascroscópico do cérebro e facies na holoprosencefalia, foram revisados seis casos examinados no Departamento de Patologia da FFFCMPA. Comparação dos dados observados neste estudo é feita com aqueles da literatura sobre o assunto.

Palavras-chave: holoprosencefalia, prosencefalia, malformações congênitas do sistema nervoso central, arrinencefalia.


SUMMARY

The aim of this study is to classify and analyse macroscopic aspects of the brain and facies in holoprosencephaly. The six cases reported were examined at the Department of Pathology of FFFCMPA. Data observed in this study are compared to those registered in the literature.

Key words: holoprosencephaly, prosencephaly, nervous system malformation, arhinencephaly.


 

 

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Aceite: 29-abril-1994.

 

 

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