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Arquivos de Neuro-Psiquiatria

Print version ISSN 0004-282X

Arq. Neuro-Psiquiatr. vol.53 no.4 São Paulo Dec. 1995

https://doi.org/10.1590/S0004-282X1995000500015 

Hemiatrofia facial de romberg. Relato de caso

 

Romberg's facial hemiatrophy: case report

 

 

Nicandro De Figueiredo NetoI; Johnny Wesley G. MartinsI; Miguel Farage FilhoII; Fernando Guilhon HenriquesIII

IHospital de Base do Distrito Federal:Médico Residente da Unidade de Neurocirurgia
IIHospital de Base do Distrito Federal:Chefe da Unidade de Neurocirurgia
IIIHospital de Base do Distrito Federal:Chefe da Unidade de Neurologia

 

 


RESUMO

Os autores apresentam o caso de uma paciente de 45 anos de idade com história de 15 meses de evolução, de hemiatrofia progressiva da face e língua à esquerda. A investigação laboratorial e de imagens foi normal, incluindo exames de sangue de rotina, líquido cerebro-espinhal, provas de função hepática, renal e reumáticas; além de raio X, tomografia computadorizada e ressonância magnética de crânio. A eletroneuromiografia mostrou alterações neurogênicas periféricas dos nervos trigêmio motor e hipoglosso, predominantemente à esquerda. Esses achados são compatíveis com o diagnóstico de hemiatrofia facial de Romberg, motivando a discussão de diversos aspectos desta rara doença de acordo com o relato e com a literatura.

Palavras-chave:hemiatrofia facial, síndrome de Parry-Romberg, doença de Romberg.


SUMMARY

The authors report the case of a 45-years-old female patient, with progressive hemiatrophy of the left face and tongue. The laboratorial and image studies were normal, including routine blood exams, cerebral-spinal fluid, hepatic function tests, renal and rheumatic; besides X ray, computerized tomography and magnetic resonance of skull. The electroneuromyography showed peripheral neurogenic alterations of motor trigeminal and hypoglossal nerves, markedly on the left side. Those findings are compatible with Romberg's facial hemiatrophy diagnosis, motivating discussion of several aspects of this rare disease according to the account and literature.

Key words:facial hemiatrophy, Parry-Romberg syndrome, Romberg's syndrome.


 

 

Texto completo disponível apenas em PDF.

Full text available only in PDF format.

 

 

Agradecimentos - Ao Dr. Tito Lívio Mundim (Clínica Villas Boas), pela realização da ressonância magnética de crânio.

 

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Aceite: 14-agosto-1995.

 

 

Dr. Nicandro de Figueiredo Neto - SQS 113, Bloco C, Apto 106 - 70373-030 Brasília DF - Brasil.

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