Steatocystoma multiplex suppurativa: case report of a rare condition* * Study conducted at Hospital Universitário Pedro Ernesto of the Universidade do Estado do Rio de Janeiro (HUPE-UERJ) – Rio de Janeiro (RJ), Brazil.

Cândida Naira Lima e Lima Santana Daniele do Nascimento Pereira Alice Paixão Lisboa Juliana Martins Leal Daniel Lago Obadia Roberto Souto da Silva About the authors

Abstract

Steatocystoma multiplex is a rare genetic disorder characterized by the presence of hamartomatous malformations at the junction of the pilosebaceous duct. It consists of encapsulated cystic lesions in the dermis, with adjacent sebaceous gland. When associated with inflammation, resembling hidradenitis, it is called steatocystoma multiplex suppurativa, a condition rarely reported. This is the first case of steatocystoma multiplex suppurativa reported in the Brazilian literature. Female patient, 23 years old, with papular and nodular cystic lesions that started in the armpits and groin, later spreading to the trunk, lower limbs, anticubital fossa, face and scalp. The presence of papular-nodular lesions associated with disseminated hidradenitis-like lesions in flexural areas and the histopathological diagnosis of steatocystoma defined the diagnosis of steatocystoma multiplex suppurativa.

Keywords:
Steatocystoma Multiplex; Hidradenitis Suppurativa; Suppuration

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