Clouston Syndrome: 25-year follow-up of a patient* * Study carried out at Faculdade de Medicina de São José do Rio Preto (FAMERP) - São José do Rio Preto (SP), Brazil.

Lívia Arroyo Trídico João Roberto Antonio Eurides Maria de Oliveira Pozetti Ana Maria Mendes Rosa Carlos Roberto Antonio About the authors

Abstract:

Clouston syndrome is a rare genodermatosis that affects skin and annexes. It is a form of ectodermal dysplasia characterized by generalized hypotrichosis, palmoplantar hyperkeratosis and nail dystrophy. This paper reports a 25-year follow-up of a patient with Clouston syndrome, from childhood to adulthood, monitoring diagnosis and clinical course of the disease.

Keywords:
Ectodermal dysplasia; Hypotrichosis; Keratoderma, palmoplantar

Sociedade Brasileira de Dermatologia Av. Rio Branco, 39 18. and., 20090-003 Rio de Janeiro RJ, Tel./Fax: +55 21 2253-6747 - Rio de Janeiro - RJ - Brazil
E-mail: revista@sbd.org.br