Clouston Syndrome: 25-year follow-up of a patient* * Study carried out at Faculdade de Medicina de São José do Rio Preto (FAMERP) - São José do Rio Preto (SP), Brazil.

Lívia Arroyo Trídico João Roberto Antonio Eurides Maria de Oliveira Pozetti Ana Maria Mendes Rosa Carlos Roberto Antonio About the authors


Clouston syndrome is a rare genodermatosis that affects skin and annexes. It is a form of ectodermal dysplasia characterized by generalized hypotrichosis, palmoplantar hyperkeratosis and nail dystrophy. This paper reports a 25-year follow-up of a patient with Clouston syndrome, from childhood to adulthood, monitoring diagnosis and clinical course of the disease.

Ectodermal dysplasia; Hypotrichosis; Keratoderma, palmoplantar

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