Wegener granulomatosis (WG) is characterized by a classic triad of granulomatous inflammation of the respiratory tract, necrotizing vasculitis and nephritis. The absence of renal disease defines a subset of " limited WG" . Approximately 50% of WG patients develop ophthalmic disease. The histopatological study and +c-ANCA were essential to make a definite diagnosis in these cases.
Wegener granulomatosis; Wegener granulomatosis; Vasculitis; Antibodies, antineutrophil cytoplasmic; Granuloma, plasma cell, orbital; Immunosuppresive agents; Case reports