Purpose: To describe the clinicopathological findings of a case of Melkersson-Rosenthal syndrome with monosymptomatic presentation. Methods: Review of the clinical chart and histopathological slides of the case. Results: The clinical diagnosis of Melkersson-Rosenthal syndrome was suspected by the presence of unilateral bipalpebral edema. The orbital computed tomography disclosed tissue thickening of both superior lids. Granulomatous lymphangitis was demonstrated histopathologically. The granulomas were present in the neighborhood and in the lumen of the lymphatic vessels. Conclusions: Melkersson-Rosenthal syndrome can occur in a monosymptomatic presentation. The histopathological demonstration of granulomatous lymphangitis confirmed the diagnosis. Systemic steroid therapy was efficient reducing the edema of the lids.
Melkersson-Rosenthal syndrome; Melkersson-Rosenthal syndrome; Edema; Eyelids; Lymphangitis; X-ray tomography computed; Adrenal cortex hormones
