1 |
F |
6 |
nephritic syndrome, hemoptysis, CKD |
1461 |
c-Anca + Tu |
n/a |
CS, CFM |
2 |
F |
1 |
Hemoptysis, nephritic syndrome, AKI, purpura, sinusitis, mastoiditis, acral necrosis |
816 |
c-Anca + 1:80 |
n/a |
CS, CFM |
3 |
F |
3.5 |
sinusitis, scleritis, multiple mononeuritis, pulmonary nodule, polyneuropathy, CHF, nephritic syndrome; AKI |
3760 |
c-Anca + Tu |
Pulmonary nodule: granulomatous vasculitis with OP |
CS, CFM, RTX |
4 |
M |
6 |
laryngitis, sinusitis, pulmonary nodule, hemoptysis, upper respiratory tract stenosis |
150 |
c-Anca + 1:320 |
n/a |
CS, CFM, RTX |
5 |
F |
66 |
sinusitis, polyarthritis, purpura laryngitis, bronchial stenosis |
130 |
c-Anca - |
Skin: LCV |
CS, CFM |
6 |
F |
0.5 |
sinusitis, CKD, alveolar hemorrhage, death |
n/a |
c-Anca + 1:640 |
n/a |
CS, CFM |
7 |
F |
84 |
sinusitis, polyarthritis, saddle nose deformity, pulmonary nodule |
74 |
c-Anca - |
Nasal mucosa: granulomatous vasculitis |
CS |
8 |
F |
36 |
multiple mononeuritis, transverse myelitis, neurosensory deafness, sinusitis, uveitis, polyarthritis,, polyneuropathy, laryngitis, pulmonary nodule |
150 |
c-Anca - |
n/a |
CS, CFM, RTX |
9 |
F |
216 |
sinusitis, saddle nose deformity nephritic syndrome, polyarthritis, dialytic AKI |
n/a |
c-Anca + 1:40 |
n/a |
CS |
10 |
F |
12 |
neurosensory deafness, polyarthritis, nephrotic syndrome, nephritic syndrome, epistaxis, dialytic CKD, alveolar hemorrhage, death |
385 |
c-Anca + 1:160 |
n/a |
CS, AZA, RTX |
11 |
M |
120 |
polyarthritis, purpura; sinusitis, orbital pseudotumor, otitis media, pericardial effusion |
64 |
c-Anca + Tu |
n/a |
CS, AZA, RTX |
12 |
F |
0.5 |
polyarthritis, nephritic syndrome; epistaxis, mastoiditis, scleritis, pulmonary nodule, facial nerve paralysis, CKD, mitral insufficiency |
1680 |
c-Anca + 1:160 |
Bronchial lesion: granulomatous vasculitis |
CS, AZA |
13 |
M |
5 |
neurosensory deafness, polyneuropathy, polyarthritis, purpura, acral necrosis, nephritic syndrome; pulmonary nodule |
150 |
c-Anca + 1:640 |
Sural nerve: granulomatous vasculitis |
CS, AZA |
14 |
F |
5 |
neurosensory deafness, sinusitis, nephritic syndrome, pulmonary nodule |
1078 |
c-Anca + 1:40 |
Kidney: diffuse proliferative GN |
CS, CFM |
15 |
F |
192 |
scleritis, polyarthritis, epistaxis, orbital pseudotumor, sinusitis, hemoptysis, AKI, amaurosis |
511 |
p-Anca + 1:640 |
Kidney: acute tubular necrosis |
CS, CFM |
16 |
F |
42 |
nodular scleritis, neurosensory deafness, polyarthritis, pulmonary nodule, third-degree AVB, cutaneous nodule |
200 |
c-Anca + 1:640 |
Skin: Churg-Strauss granuloma; pulmonary nodule: granulomatous vasculitis with OP |
CS, CFM |
17 |
F |
120 |
Purpura, hemoptysis, cutaneous nodule, polyarthritis, CKD, orbital pseudotumor, |
900 |
c-Anca + 1:320 |
Nasal mucosa: granulomatous vasculitis |
CS, CFM, AZA, RTX |
18 |
F |
0.5 |
purpura, pulmonary-renal syndrome, death |
n/a |
c-Anca + 1:320 |
Skin: LCV |
CS, IMGN |
19 |
M |
1 |
polyarthritis, nephrotic syndrome, pulmonary-renal syndrome, death |
26,350 |
c-Anca + 1:80 |
Bronchial: granulomatous vasculitis |
CS, CFM, PLASMF |
20 |
F |
1 |
sinusitis, purpura, polyarthritis, nephritic syndrome |
775 |
c-Anca + 1:640 |
Kidney: FSGS |
CS, CFM, RTX |
21 |
F |
120 |
hemoptysis, otitis media, sinusitis |
140 |
c-Anca + 1:640 |
n/a |
CS, AZA, RTX |
22 |
F |
32 |
Raynaud phenomen, vertigo, polyneuropathy, purpura, sinusitis |
150 |
c-Anca + 1:20 |
Skin: LCV |
CS, AZA |
23 |
F |
3 |
polyarthritis, hemoptysis, nephritic syndrome, AKI, nephrotic syndrome |
4300 |
c-Anca + 1:160 |
Kidney: pauci-immune crescentic GN |
CS, RTX |
24 |
F |
n/a |
sinusitis, anosmia, pulmonary fibrosis |
n/a |
p-Anca + 1:640 |
n/a |
CS, CFM |
25 |
F |
3 |
Scleritis, purpura, polyarthritis, sinusitis, Cushing's syndrome |
n/a |
c-Anca + 1:80 |
Skin: LCV |
CS, MTX |