A case of intradiploic dermoid cyst of the skull in a female child with seizures is reported. The authors emphasize diagnostic aspects and the surgical procedure. The caracteristics of the tumor were cleared at the surgical procedure, and its nature was confirmed by histological examination- The importance of the skull biopsy when radiological aspects are not definite and the benign caracteristics of the process are discussed. Good results of surgical treatment and the infrequency of the tumor justify the report.