Abstracts
Chronic myelopathy associated with T-lymphotropic virus type I (HAM) has been described as an endemic disease in several areas of the world, meanwhile there are few papers describing the association between HAM and adult T cell leukemia-lymphoma. We report the case of a man that, after four years of progressive spastic paraparesis and neurogenic bladder, developed a clinical picture of a lymphoproliferative disorder characterized by dermal and systemic envolvement, mimicking mycosis fungoides/Sézary syndrome.
HTLV-I; HAM; TSP; ATLL; myelopathy; encephalomyeloneuropathy
Apesar da infecção pelo HTLV-I ser endêmica em várias regiões do mundo, poucos são os relatos da associação entre leucemia-linfoma de células T do adulto (ATLL) e encefalomieloneuropatia pelo HTLV-I. No presente artigo é descrito um paciente que no curso do comprometimento neurológico pelo HTLV-I desenvolveu quadro de leucemia com infiltração de tecido dérmico semelhante ao encontrado na micose fungóide/síndrome de Sézary.
HTLV-I; TSP; HAM; ATLL; mielopatia; encefalomieloneuropatia
Adult T-cell leukemia-lymphoma in a patient with HTLV-I/II associated myelopathy
Leucemia - linfoma de células T do adulto em um paciente com mielopatia associada a HTLV-I/II
Virgínia Freitas; Irenio Gomes; Achilea Bittencourt; Dilson Fernandes; Ailton Melo
Federal University of Bahia (UFBA)
ABSTRACT
Chronic myelopathy associated with T-lymphotropic virus type I (HAM) has been described as an endemic disease in several areas of the world, meanwhile there are few papers describing the association between HAM and adult T cell leukemia-lymphoma. We report the case of a man that, after four years of progressive spastic paraparesis and neurogenic bladder, developed a clinical picture of a lymphoproliferative disorder characterized by dermal and systemic envolvement, mimicking mycosis fungoides/Sézary syndrome.
Key words: HTLV-I, HAM, TSP, ATLL, myelopathy, encephalomyeloneuropathy.
RESUMO
Apesar da infecção pelo HTLV-I ser endêmica em várias regiões do mundo, poucos são os relatos da associação entre leucemia-linfoma de células T do adulto (ATLL) e encefalomieloneuropatia pelo HTLV-I. No presente artigo é descrito um paciente que no curso do comprometimento neurológico pelo HTLV-I desenvolveu quadro de leucemia com infiltração de tecido dérmico semelhante ao encontrado na micose fungóide/síndrome de Sézary.
Palavras-chave: HTLV-I, TSP, HAM, ATLL, mielopatia, encefalomieloneuropatia.
Texto completo disponível apenas em PDF.
Full text available only in PDF format.
Aceite: 22-fevereiro-1997.
Dr. Ailton Melo - Faculdade de Medicina UFBA - Av. Reitor Miguel Calmon s/n - 40110-100 Salvador BA - Brasil.
References
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Publication Dates
-
Publication in this collection
10 Nov 2010 -
Date of issue
June 1997