Sickle cell disease knowledge survey |
1. Among the diseases screened by the Neonatal Screening Program, which one has the highest incidence in the Brazilian population? |
() Congenital Hypothyroidism |
() Phenylketonuria |
() Sickle Cell Disease
|
() Cystic fibrosis |
() Biotinidase Deficiency |
() Congenital Adrenal Hyperplasia |
() Don’t know |
2. When discussing Sickle Cell Disease, it is CORRECT to state that |
() It occurs among the black population in Brazil |
() It is one of the rarest genetic disorders in Brazil and worldwide. |
() It is characterized by the predominance of hemoglobin S in red blood cells
|
() Its SS genotype is a mild form of the disease |
() Don’t know |
3. Which one is the Sickle Cell Anemia Genotype? |
() Hb SC |
() Hb AS |
() Hb SS
|
() Hb SD |
() Hb AA |
() Don’t know |
4. When referring to persons with Sickle Cell Trait, it is CORRECT to state that they |
() Need monitoring and hematological treatment |
() Suffer from anemia |
() Do not have a disease but a relatively common and clinically benign condition
|
() Are not advised to practice physical activity |
() Don’t know |
5. All of the following are features of Sickle Cell Disease EXCEPT FOR |
() Jaundice |
() Frequent Infections |
() Hemolytic anemia |
() Iron deficiency anemia
|
() Biliary Calculus |
() Don’t know |
6. All of the following manifestations are caused by vaso-occlusion EXCEPT FOR |
() Pain cramps |
() Priapism |
() Leg ulcers |
() Retinopathy |
() Osteonecrosis |
() Hyperglycemia
|
() Hand-Foot Syndrome (Dactylitis) |
() Stroke |
() Don’t know |
7. All of the following conditions favor the sickling of erythrocytes EXCEPT FOR |
() Dehydration |
() Strenuous physical activity |
() Exposure to cold |
() Being overweight
|
() Emotional stress |
() Don’t know |
8. All of the following signs are considered warning signs in Sickle Cell Disease EXCEPT FOR |
() Fever |
() Enlarged spleen and liver |
() Coughing or shortness of breath |
() Abdominal pain |
() Feet and leg Itching
|
() Worsening in pallor of skin and mucous membranes |
() Nausea/vomiting |
() Neurological deficit |
() Don’t know |
9. All of the following drugs are used to prevent and/or treat Sickle Cell Disease and its intercurrences EXCEPT FOR |
() Penicillin |
() Folic acid |
() Ferrous sulphate
|
() Hydroxyurea |
() Pain killers |
() Iron chelator |
() Don’t know |
10. Persons with Sickle Cell Disease should be prescribed antibiotics and guided as to how to take them in all of the following situations EXCEPT FOR |
() Children under 5 years old |
() Pregnant women
|
() In dental procedures |
() In case of presumed infection |
() Don’t know |
11. In the case of teenagers with Sickle Cell Disease, it is INCORRECT to state that |
() They will generally experience delayed growth and puberty |
() They are prone to develop self-concept, self-image and self-esteem disorders |
() Priapism in male teenagers is always related to sexual desire
|
() They may have academic and professional skills deficits |
() Don’t know |
12. As regards pregnancy and contraception in persons with Sickle Cell Disease, it is CORRECT to state that |
() Urinary and respiratory tract infections are uncommon |
() Pregnancy is a potentially serious condition for woman and fetus
|
() Women with sickle cell disease must be advised against becoming pregnant |
() Pre-natal care must be done at a Primary Care Unit |
() Women with sickle cell disease must not be on injectable or oral contraceptives |
() Don’t know |
13. All of the following are recommended guidelines for preventing leg ulcers in persons with Sickle Cell Disease EXCEPT FOR |
() Skin nourishing and cleansing |
() Use of adequate and comfortable footwear |
() Use of insect repellents and insect bite treatment |
() Mandatory use of compression stockings
|
() Do not know |