Endovascular treatment of an aneurysm of the brachiocephalic trunk in a patient with Ehlers-Danlos syndrome type IV

Sergio Quilici Belczak Rafael Kogan Klajner Lara Cote Ogawa Laís Leite Lucato Bruna Stecca Zeque Felipe Basso de Macedo Ingredy Tavares da Silva Luís Felipe Atihe About the authors

Abstract

Ehlers-Danlos syndrome is a genetic disease that results in abnormalities of collagen synthesis, causing extremely fragile connective tissue. This fragility predisposes patients to a series of vascular disorders, such as dissections, aneurysms and pseudoaneurysms. The authors describe the case of a 19-year-old patient with an aneurysm of the brachiocephalic trunk who was treated endovascularly by placement of covered stents. The case progressed with complications at the puncture site, which was also treated on an emergency basis, using endovascular techniques with a covered stent.

Keywords:
aneurysm; brachiocephalic trunk; Ehlers-Danlos syndrome

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